Nefromegalia

A newborn female infant with marked bilateral renal enlargement resulting from an absolute increase in renal parenchymal mass is described. The number of renal lobes was increased and there was persistent subcapsular glomerulogenesis. In addition, the lungs manifested delayed maturation and contained multiple small cysts. Although the renal growth disturbance resembled that sometimes found in hemihypertrophy and the Beckwith syndrome, the associated pulmonary lesions and the absence of other anomalies make this patient distinctive...

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No abstract text is available yet for this article.

Hemihypertrophy is associated with malignant visceral abdominal neoplasms in childhood. Benign nephromegaly and nephroblastomas are both known to occur with hemihypertrophy; however, association with renal dysplasia has not previously reported. We describe an infant presenting with recurrent haematuria who had segmental hemihypertrophy, ipsilateral renal dysplasia and contralateral benign nephromegaly. Although debated, renal dysplasia may predispose to and predate malignant change. Rational management and optimal surveillance of renal dysplasia and benign nephromegaly in hemihypertrophy is discussed...

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