Unusual complicated fungal endocarditis in a patient with vascular Ehlers-Danlos Syndrome.

A 24-year-old man with dilated aortic root and vascular type Ehlers-Danlos Syndrome underwent aortic root replacement with a stentless bioprosthesis. A year later he developed aortic valve endocarditis necessitating a redo valve replacement. Excised valve tissue grew fungus Purpureocillium lilacinum. Over a period of four years case was further complicated with mycotic aneurysm of the infra-renal aorta, a retroperitoneal abscess (treated surgically), a right common iliac aneurysm, right lower limb emboli (femoral embolectomy and left -to-right femoral bypass was performed), two false aneurysms of the ascending aorta with a large mobile mass attached to the anterior aneurysm and brain abscesses.