Left atrial low-voltage zone ablation of persistent atrial fibrillation in a patient with myotonic dystrophy: A case report.

We here report a case of a 32-year-old man with genetically diagnosed myotonic dystrophy and persistent atrial fibrillation (AF) who underwent a low-voltage zone (LVZ) ablation. His cardiac function was normal except for a prophylactic pacemaker implantation for a high risk of complete atrioventricular block. An LVZ was found in the anteroseptal left atrium during sinus rhythm and was ablated during induced AF after a pulmonary vein antrum isolation, which terminated the AF and rendered it noninducible by rapid pacing and/or isoproterenol. During 20 months of follow-up, no atrial tachyarrhythmias were observed with pacemaker monitoring of antiarrhythmic drugs.