Multimodal imaging in a case of butterfly pattern dystrophy of retinal pigment epithelium.

AIMS: To report multi-modal imaging findings in a case of butterfly pattern dystrophy of retinal pigment epithelium.

METHODS: A middle-aged female with butterfly pattern dystrophy, who presented with progressive loss of vision, was examined using coloured fundus photographs, short wave autofluorescence, swept source optical coherence tomography (SS-OCT), fundus fluorescein angiography and enface optical coherence tomography.

RESULTS: Multi-modal imaging was useful in the characterization of the various disease features. Autofluorescence pattern was opposite to that of fluorescein angiogram and SS-OCT showed disruption in the outer retinal layers. Enface OCT images depicted the pigment deposition prominently.

CONCLUSION: The features of butterfly pattern dystrophy on these modalities correlated well with the histopathological findings described in the literature. Enface imaging highlights the deposition of pigment/lipofuscin and has never been described in BPD.