A rare atypical rapidly involuting congenital hemangioma combined with vascular malformation in the upper limb.

BACKGROUND: Rapidly involuting congenital hemangioma is a congenital soft tissue tumor, which is difficult to excise completely and rather prone to recur. This atypical tumor combined with capillary-lymphatic-venous malformation was not reported in the literature.

CASE PRESENTATION: We report an atypical case of a 16-year-old teenager who was born with a mass in his right upper limb. Since there is a recurrence after excision for several times and had a serious impact on daily life, we chose amputation. After the surgery, the patient gained a functional recovery. Two years after the surgery, he had no tumor recurrence.

CONCLUSIONS: For this rare tumor with repeated recurrences and significant impact on daily life, we suggest performing amputation at the early stage.