[New advances in the management and treatment of cystic fibrosis].

Cystic fibrosis represented and continue to represent either for the system and for the practitioner a serious challenge through the severe manifestations of disease, progressive mainly in the lung, through the progres in the management registrated in the last time for fighting lung infections such as Pseudomonas aeruginosa, in understanding of genetic condition, new ways of administration of antibiotics and the problems posed by today transition of these patients from pediatrician to the pulmonologist, infectious disease specialist, rehabilitation specialist etc. There have been noted extensions of survival and improvement of diagnostic rate. Today in France in the Caucasian population, there were 6,000 cases with this common disease, of which half were adults (> 18 years). I'll review a number of novelties reported last year connected to this disease adding recent signals received after the congress organized by the North American Cystic Fibrosis Foundation in October 2013 in North Lake City that maybe in the future will extend the duration of survival of these patients.