Alessio Gasperetti, Giovanni Peretto, Steven A Muller, Kanae Hasegawa, Paolo Compagnucci, Michela Casella, Brittney Murray, Crystal Tichnell, Richard T Carrick, Julia Cadrin-Tourigny, Marco Schiavone, Cynthia James, Ahmad S Amin, Ardan M Saguner, Antonio Dello Russo, Claudio Tondo, William Stevenson, Paolo Della Bella, Hugh Calkins, Harikrishna Tandri
BACKGROUND: Desmoplakin (DSP) pathogenic/likely pathogenic (P/LP) variants are associated with malignant phenotypes of arrhythmogenic cardiomyopathy (DSP-ACM). Reports of outcomes after ventricular tachycardia (VT) ablation in DSP-ACM are scarce. OBJECTIVES: In this study, the authors sought to report on long-term outcomes of VT ablation in DSP-ACM. METHODS: Patients with P/LP DSP variants at 9 institutions undergoing VT ablation were included...
December 14, 2023: JACC. Clinical Electrophysiology