Tomas Simurda, Rita Marchi, Alessandro Casini, Marguerite Neerman-Arbez, Miroslava Drotarova, Ingrid Skornova, Jana Zolkova, Zuzana Kolkova, Dusan Loderer, Monika Brunclikova, Kristina Maria Belakova, Jan Stasko
Rotational thromboelastometry (ROTEM) is a global hemostasis assay. The diagnosis added value of ROTEM in congenital dysfibrinogenemia remains to be established. The aim of this study was to analyze clot formation by ROTEM in a cohort of dysfibrinogenemic patients and to establish correlations with genotype, clinical features, and coagulation parameters. The study included genetically confirmed congenital dysfibrinogenemia cases (n = 63) and healthy controls ( n = 50). EXTEM, INTEM, FIBTEM tests were used to measure ROTEM parameters, that is, clotting time (CT), clot formation time (CFT), maximal clot firmness (MCF) and amplitude 10 min after CT (A10)...
March 1, 2024: Blood Coagulation & Fibrinolysis: An International Journal in Haemostasis and Thrombosis