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Prune belly syndrome

Ganavi Ramagopal, Ganesh Narayana, Ashok Rathod
No abstract text is available yet for this article.
July 2016: Journal of Neonatal Surgery
Karim Awad, Anupam Lall
Prune belly syndrome is a rare abnormality; its association with VACTERL is even rarer. This association has been reported in literature a few times since first reported in 1993 and so far the majority have either been stillbirths or died shortly after birth. We present a case of Prune belly syndrome associated with VACTERL who is now one year old.
July 2016: Journal of Neonatal Surgery
Romain Boissier, Eugenie Di Crocco, Alice Faure, Geraldine Hery, Véronique Delaporte, Eric Lechevallier, Pierre D E Mouriquand, Jean-Michel Guys, Gilles Karsenty
OBJECTIVE: To document the long-term outcomes of paediatric augmentation gastrocystoplasty (AGC) in terms of preservation of renal function and maintenance of dryness, and to analyse the rate of complications. PATIENTS AND METHODS: The medical records of children who had undergone AGC between 1992 and 2000 (minimum time interval of 15 years) were reviewed retrospectively. The following data were collected: age at surgery, the cause of bladder dysfunction, functioning of the AGC, any complications, and the long-term outcome of the patients...
June 20, 2016: BJU International
Herman S Bagga, Songhua Lin, Alun Williams, Jesse Schold, Nathan Chertack, David Goldfarb, Hadley Wood
PURPOSE: Improved bladder and renal management benefit patients with congenital uropathy and congenital pediatric kidney disease. This may translate to delayed initial renal transplantation in these patients, and improved graft and patient survival. Our primary study purpose was to determine whether patients with congenital uropathy and congenital pediatric kidney disease have demonstrated later time to first transplantation and/or graft survival. MATERIALS AND METHODS: SRTR (Scientific Registry of Transplant Recipients) was analyzed for first renal transplant and survival data in patients with congenital uropathy and congenital pediatric kidney disease from 1996 to 2012...
April 2016: Journal of Urology
Michael P Leonard
No abstract text is available yet for this article.
April 2016: Journal of Pediatric Urology
M L Garcia-Roig, J D Grattan-Smith, A M Arlen, E A Smith, A J Kirsch
INTRODUCTION: Magnetic resonance urography (MRU) has proven to be useful in the setting of complex urologic anatomy. Prune belly syndrome (PBS) patients are known to have malformed and highly variable urinary tract anatomy due to significant dilation and renal dysplasia. OBJECTIVE: To further characterize the renal and ureteral anatomy and renal function in patients with PBS via MRU. STUDY DESIGN: Children with PBS undergoing MRU (2006-2011) were identified...
April 2016: Journal of Pediatric Urology
Laura Travan, Samuele Naviglio, Gabriele Cont, Pierpaolo Brovedani, Riccardo Davanzo, Sergio Demarini
We report the case of an infant born after parvovirus B19-induced fetal hydrops, who presented at birth with bilateral abdominal wall laxity, which was more evident on the flanks. Imaging exams revealed congenital hypoplasia of oblique abdominal muscles not associated with other anatomical abnormalities except for small liver calcifications. We review the medical literature and identify similar cases associated with fetal ascites. We propose that isolated hypoplasia of abdominal wall muscles can be associated with fetal ascites from various causes, and represents a separate condition from prune belly syndrome...
July 2016: Congenital Anomalies
Malik Mahmood Alam
No abstract text is available yet for this article.
July 2015: Journal of Ayub Medical College, Abbottabad: JAMC
J Sánchez Catalicio, M Gallego Peinado, F Pérez Angel, M T Martinez Martínez, J D González Rodríguez, J F Contreras Gutiérrez
No abstract text is available yet for this article.
July 2016: Revista Española de Medicina Nuclear e Imagen Molecular
Angela M Arlen, Susan S Kirsch, Natan E Seidel, Michael Garcia-Roig, Edwin A Smith, Andrew J Kirsch
OBJECTIVE: To compare health-related quality of life (HRQoL) in children with prune-belly syndrome (PBS) and their caregivers to healthy controls, as children and adolescents with PBS face numerous potential physical and psychosocial challenges. MATERIALS AND METHODS: Study participants completed the Pediatric Quality of Life Inventory Generic Core Scales (PedsQL) 4.0 generic core scales (children) or Quality of Life Enjoyment and Satisfaction Questionnaire Short Form (Q-LES-Q-SF) (caregivers) in an online, anonymous format...
January 2016: Urology
Bin Liu, Summer L Kaplan, Hongming Zhuang
Patients with prune belly syndrome usually have tortuous ureters, which can cause difficulty in the interpretation of renal scan used to evaluate possible urine leak after renal transplant. We reported a renal scan finding in a pediatric renal transplant patient with prune belly syndrome. The radioactivity in the dilated ureter, which was lateral to the renal transplant, appears to be urine leak.
March 2016: Clinical Nuclear Medicine
Ismail R Saad, Enmar Habib, Mohammed S ElSheemy, Mahmoud Abdel-Hakim, Mostafa Sheba, Aziz Mosleh, Doaa M Salah, Hafez Bazaraa, Fatina I Fadel, Hany A Morsi, Hesham Badawy
OBJECTIVES: To compare outcomes of renal transplantation (RTx) in children with end-stage renal disease (ESRD) resulting from lower urinary tract dysfunction (LUTD) vs other causes. PATIENTS AND METHODS: A database of children (<18 years old) who underwent RTx between May 2008 and April 2012 was reviewed. Patients were divided into those with LUTD (group A, n = 29) and those with other causes of ESRD (group B, n = 74). RTx was performed after achieving low intravesical pressure (<30 cmH2 O) with adequate bladder capacity and drainage...
August 2016: BJU International
L Legros, N Revencu, M-C Nassogne, F-X Wese, A Feyaerts
We report on the case of a child who presented with recurrent, multiple, and voluminous bladder diverticula. Bladder diverticula are defined as a herniation of the mucosa through the bladder muscle or the detrusor. Causes are numerous and diverticula can be classified into primary congenital diverticula (para-ureteral - or Hutch diverticula - and posterolateral diverticula); secondary diverticula (resulting from chronic mechanical obstruction or from neurological disease; and diverticula secondary to connective tissue or muscle fragility...
November 2015: Archives de Pédiatrie: Organe Officiel de la Sociéte Française de Pédiatrie
Rodrigo Romao
No abstract text is available yet for this article.
October 2015: Journal of Pediatric Urology
G M Grimsby, S M Harrison, C F Granberg, I H Bernstein, L A Baker
INTRODUCTION: Prune belly syndrome (PBS) extra-genitourinary (extra-GU) manifestations are serious comorbidities beyond the genitourinary (GU) anomalies of this disease. We hypothesized an underestimation of the reported frequency and understated impact on quality of life (QOL) of extra-GU comorbidities in PBS survivors beyond the newborn period. To assess this, the frequencies of extra-GU manifestations of PBS in a contemporary cohort of living patients were compared to compiled frequencies from published literature...
October 2015: Journal of Pediatric Urology
F T Dénes, R Park, R I Lopes, P R M Moscardi, M Srougi
INTRODUCTION: Many patients with Prune Belly Syndrome (PBS) require abdominoplasty alone or in combination with correction of any urogenital abnormalities. This video presents a simplified technique with which to treat the abdominal flaccidity in PBS. METHODS: A longitudinal xypho-pubic fusiform figure is drawn on the abdomen, based on the area of skin and subcutaneous tissue to be removed. This is performed with preservation of the musculo-fascial layer and the umbilicus...
October 2015: Journal of Pediatric Urology
Nina Kimmich, Christian Haslinger, Martina Kreft, Roland Zimmermann
Diastasis recti abdominis during pregnancy is a frequent phenomenon with a prevalence of 30–70%. It is associated with functional and cosmetic limitations. Gold standard in diagnosis during pregnancy is the transabdominal ultrasonography. The most frequent localization is in the periumbilical region and persistence postpartum is found in about 60% of cases. Either conservative or surgical treatments seem to be effective, but relapse rates, especially after surgical therapy, are unclear. It is a problem that no standard values of diastasis recti are given, no evidence-based therapy schemes are implemented and only rare and insufficient studies exist...
July 22, 2015: Praxis
Grahame H H Smith
No abstract text is available yet for this article.
October 2015: Journal of Pediatric Urology
R I Lopes, A Tavares, M Srougi, F T Dénes
INTRODUCTION: Prune belly syndrome (PBS) presents with three main features: abdominal wall flaccidity, urological abnormalities and cryptorchidism. As a result, urologists must consider the eventual repair of the abdominal wall flaccidity and urinary tract abnormalities, and the mandatory correction of cryptorchidism, as well as decide whether to perform the procedures in a single comprehensive approach or in multiple steps. OBJECTIVES: To report experiences with comprehensive surgical management of prune belly syndrome...
October 2015: Journal of Pediatric Urology
Wendy Whiteside, Jason Christensen, Jeffrey D Zampi
Multimodality image overlay is increasingly used for complex interventional procedures in the cardiac catheterization lab. We report a case in which three-dimensional magnetic resonance imaging (3D MRI) overlay onto live fluoroscopic imaging was utilized to safely obtain transhepatic access in a 12-year-old patient with prune belly syndrome, complex and distorted abdominal anatomy, and a vascular mass within the liver.
May 2015: Annals of Pediatric Cardiology
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