Lu Zhang, Yu-Jun Dong, Hong-Ling Peng, Hao Li, Ming-Zhi Zhang, Hui-Han Wang, Qin-Hua Liu, Li-Ping Su, Li-Ye Zhong, Wen-Jun Wu, Liang Huang, Xiao-Jing Yan, Lei Fan, Wen-Jiao Tang, Zhen-Ling Li, Lin-Tao Bi, Yan Li, Guang-Xun Gao, Li Gao, Ting-Bo Liu, Yong-Qiang Wei, Yao Liu, Li Yu, Hui Zhou, Chun-Yan Sun, Wen-Bin Qian, De-Hui Zou, Hui-Lai Zhang, Kai-Yang Ding, Xiao-Bo Wang, Ou Bai, Wen-Rong Huang, Bing Chen, Lin Yang, Jia Song, Da Gao, Tong Chen, Jun Luo, Shu-Ye Wang, Liang-Ming Ma, David C Fajgenbaum, Jian Li
BACKGROUND: Castleman disease (CD) is a group of rare and heterogenous lymphoproliferative disorders including unicentric CD (UCD), human herpesvirus-8(HHV-8)-associated multicentric CD (HHV8-MCD), and HHV-8-negative/idiopathic multicentric CD (iMCD). Knowledge of CD mainly comes from case series or retrospective studies, but the inclusion criteria of these studies vary because the Castleman Disease Collaborative Network (CDCN) diagnostic criteria for iMCD and UCD were not available until 2017 and 2020, respectively...
May 2023: The Lancet Regional Health. Western Pacific