Omer Karadag, Ertugrul Cagri Bolek, Gizem Ayan, Aladdin J Mohammad, Peter C Grayson, Christian Pagnoux, Eduardo Martín-Nares, Sara Monti, Yoshiyuki Abe, Federico Alberici, Fatma Alibaz-Oner, David Cuthbertson, Lorenzo Dagna, Haner Direskeneli, Nader A Khalidi, Curry Koening, Carol A Langford, Carol A McAlear, Paul A Monach, Luca Moroni, Roberto Padoan, Phillip Seo, Kenneth J Warrington, Alojzija Hocevar, Andrea Hinojosa-Azaola, Shunsuke Furuta, Giacomo Emmi, Seza Ozen, David Jayne, Peter A Merkel
OBJECTIVE: We describe the demographics, clinical features, disease course, and survival of polyarteritis nodosa (PAN) through an international collaboration (GLOBAL-PAN). METHODS: Patients with PAN were recruited between 1990 and 2020 from observational cohorts of nine countries across Europe, Japan, and North America. Eligibility was retrospectively defined using the European Medicines Agency classification algorithm. Patients with PAN related to hepatitis B virus (n = 12) and two monogenic diseases mimicking PAN, deficiency of adenosine deaminase 2 enzyme (n = 16) or familial Mediterranean fever (n = 11), were excluded...
February 12, 2024: Arthritis & Rheumatology