Hiroshi Shimizu, Shuzo Sato, Tomohiro Suzuki, Tomomi Sasajima, Yosuke Takahata, Nobuhiko Shinohara, Kosuke Hideshima, Yuko Yokokawa, Nobuo Matsuhashi, Osamu Ichii, Mayumi Tai, Yutaka Ejiri, Kiori Yano, Takayuki Ikezoe, Hiromasa Ohira, Kiyoshi Migita
BACKGROUND: Gastrointestinal lesions, which sometimes develop in Behçet's disease (BD), are referred to as intestinal BD. Although rare, intestinal BD can be accompanied by myelodysplastic syndrome (MDS) with abnormal karyotype trisomy 8, which is refractory to immunosuppressive therapy. Pulmonary alveolar proteinosis is a rare lung complication of BD and MDS. Herein, we present an extremely rare case of intestinal BD presenting with MDS and several chromosomal abnormalities, followed by secondary pulmonary proteinosis...
December 20, 2021: BMC Gastroenterology