keyword
https://read.qxmd.com/read/38431519/bidirectional-approach-of-vascular-access-for-balloon-angioplasty-in-permcath-associated-superior-vena-cava-syndrome-presenting-with-transudative-chylothorax
#1
JOURNAL ARTICLE
Tzu-Ching Lin, Hsuen-En Huang, Chien-An Liu, Man-Yu Na, Hsin-Lin Tsai, Jei-Wen Chang
No abstract text is available yet for this article.
February 23, 2024: Pediatrics and Neonatology
https://read.qxmd.com/read/37808560/case-report-blotchy-skin-in-a-puffy-neonate-is-there-a-new-association
#2
Chacko J Joseph, Arijit Lodha, Soumya R Thomas, Essa Al Awad, Nicola A M Wright, Cora Constantinescu, Doan Le, Majeeda Kamaluddeen
INTRODUCTION: Purpura fulminans in the neonatal population is a rare but potentially life-threatening condition complicated by thrombosis, resultant vital organ necrosis, and gangrene of the extremities. Considering the rapid evolution of the pathogenetic mechanism, an index of suspicion, early identification, and prompt intervention are imperative for improved outcomes. The majority of purpura fulminans cases have an infectious etiology, but it is essential to consider other congenital and acquired causes...
2023: Frontiers in Pediatrics
https://read.qxmd.com/read/37274623/case-report-of-generalized-lymphatic-dysplasia-with-piezo1-mutation-and-review-of-the-literature
#3
Wedad Alhazmi, Afnan Qurban, Essa Alrashidi
BACKGROUND: The newborn malformation of primary lymphatic dysplasia (PLD), developed primarily due to PIEZO1 gene autosomal recessive mutation, is known to hinder with the lymphatic system action, causing chyle or lymph effusion into the peritoneal cavity or pleura. CASE PRESENTATION: A 4-years-old male subject presented with a recurrent chylothorax and bilateral lower limb edema that started at age of 6 months. Lymphoscintigraphy showed lymphangiectasia with chylothorax...
2023: Respiratory Medicine Case Reports
https://read.qxmd.com/read/37040015/neonatal-lymphatic-flow-disorder
#4
JOURNAL ARTICLE
Handan Hakyemez Toptan, Elif Ozalkaya, Nilgun Karadag, Sevilay Topcuoglu, Emre Dincer, Guner Karatekin
OBJECTIVE: To examine and discuss patients diagnosed with acquired and congenital chylothorax in the neonatal period in the light of the literature. METHODS: The files of newborns followed-up in the neonatal intensive care unit (NICU) and diagnosed with congenital and acquired chylothorax were reviewed retrospectively. Patients with isolated chylothorax were classified as Group 1 and those with multiple lymphatic flow disorders were classified as Group 2. Antenatal and clinical features were recorded and compared between the groups...
April 11, 2023: Indian Journal of Pediatrics
https://read.qxmd.com/read/37035393/a-case-report-of-successful-therapy-for-neonatal-chylothorax-with-pneumothorax-by-conservative-medical-treatment
#5
Chunyan Zhang, Yun Pang
BACKGROUND: Neonatal chylothorax is a rare disease that causes breathing difficulties in newborns and is one of the most common causes of pleural effusion during the neonatal period. Neonatal chylothorax is often caused by lymph leakage into the chest and can be divided into the following 5 types: congenital chylothorax, traumatic chylothorax, postoperative chylothorax, embolic chylothorax, and spontaneous chylothorax. Among them, spontaneous chylothorax is the most common type of neonatal chylothorax and has unknown causes...
March 31, 2023: Translational Pediatrics
https://read.qxmd.com/read/36980822/prenatal-clinical-findings-in-rasa1-related-capillary-malformation-arteriovenous-malformation-syndrome
#6
JOURNAL ARTICLE
Emanuele Coccia, Lara Valeri, Roberta Zuntini, Stefano Giuseppe Caraffi, Francesca Peluso, Luca Pagliai, Antonietta Vezzani, Zaira Pietrangiolillo, Francesco Leo, Nives Melli, Valentina Fiorini, Andrea Greco, Francesca Romana Lepri, Elisa Pisaneschi, Annabella Marozza, Diana Carli, Alessandro Mussa, Francesca Clementina Radio, Beatrice Conti, Maria Iascone, Giancarlo Gargano, Antonio Novelli, Marco Tartaglia, Orsetta Zuffardi, Maria Francesca Bedeschi, Livia Garavelli
Pathogenic variants in RASA1 are typically associated with a clinical condition called "capillary malformation-arteriovenous malformation" (CM-AVM) syndrome, an autosomal dominant genetic disease characterized by a broad phenotypic variability, even within families. In CM-AVM syndrome, multifocal capillary and arteriovenous malformations are mainly localized in the central nervous system, spine and skin. Although CM-AVM syndrome has been widely described in the literature, only 21 cases with prenatal onset of clinical features have been reported thus far...
February 22, 2023: Genes
https://read.qxmd.com/read/36646910/chylothorax-in-newborns-after-cardiac-surgery-a-rare-complication
#7
JOURNAL ARTICLE
Alba Pérez-Pérez, Sara Vigil-Vázquez, Ana Gutiérrez-Vélez, Gonzalo Solís-García, María López-Blázquez, Jose Luis Zunzunegui Martínez, Constancio Medrano López, Juan Miguel Gil-Jaurena, Juan Carlos de Agustín-Asensio, Manuel Sánchez-Luna
UNLABELLED: The aim of this study was to analyze patients diagnosed with chylothorax after congenital heart disease surgery among a cohort of neonatal patients, comparing the evolution, complications, and prognosis after surgery of patients who were and were not diagnosed with chylothorax, and to analyze possible risk factors that may predict the appearance of chylothorax in this population. Retrospective and observational study included all neonates (less than 30 days since birth) who underwent congenital heart disease surgery in a level III neonatal intensive care department...
January 17, 2023: European Journal of Pediatrics
https://read.qxmd.com/read/36507120/outcome-of-newborns-with-tracheoesophageal-fistula-an-experience-from-a-rapidly-developing-country-room-for-improvement
#8
JOURNAL ARTICLE
Amal Al-Naimi, Sara G Hamad, Abdalla Zarroug
METHODS: This is a retrospective review of the medical electronic charts of patients with TEF that were followed at Sidra Medicine in the state of Qatar. The review included the patients who were operated upon in the period of 2011-2021 but continued to follow at our institution in the period of 2018-2021. Demographic data, associated anomalies, preoperative, operative, and postoperative courses, and growth parameters were collected. RESULTS: A total of 35 patients with TEF (24 males and 11 females) were collected...
2022: Pulmonary Medicine
https://read.qxmd.com/read/35708392/successful-thoracoscopic-resection-of-a-giant-mediastinal-cyst-in-a-newborn-boy
#9
Zhongwen Li, Weike Xie, Chaoxiang Lu, Qi Wang
There are fewer reports of thoracoscopic surgical resection of mediastinal cysts in neonates. The aim of this article is to report on the feasibility of thoracoscopic resection of a large mediastinal cyst and the management of chylothorax after surgery in neonates.
July 2022: Journal of Minimal Access Surgery
https://read.qxmd.com/read/34891190/vena-cava-thrombosis-after-congenital-diaphragmatic-hernia-repair-multivariate-analysis-of-potential-risk-factors
#10
JOURNAL ARTICLE
Rim Kiblawi, Christoph Zoeller, Sabine Pirr, Alejandro D Hofmann, Benno Ure, Jens Dingemann
INTRODUCTION:  The treatment of newborns with congenital diaphragmatic hernia (CDH) is associated with a significant complication rate. Information on major thrombotic complications and their incidence in newborns with CDH is lacking. The aims of our analysis were to evaluate the frequency of vena cava thrombosis and to determine its predictors within a consecutive series of patients with CDH. MATERIALS AND METHODS:  We retrospectively analyzed charts of all neonates of our department that underwent CDH repair from 2007 to 2021, focusing on vena cava thrombosis...
December 10, 2021: European Journal of Pediatric Surgery
https://read.qxmd.com/read/34515211/congenital-chylothorax-of-the-newborn-a-systematic-analysis-of-published-cases-between-1990-and-2018
#11
Bernhard Resch, Gülsen Sever Yildiz, Friedrich Reiterer
BACKGROUND: Congenital chylothorax (CCT) of the newborn is a rare entity but the most common cause of pleural effusion in this age-group. We aimed to find the optimal treatment strategy. MATERIAL AND METHODS: A PubMed search was performed according to the PRISMA criteria. All cases were analyzed according to prenatal, perinatal, and postnatal treatment modalities and follow-ups. RESULTS: We identified 753 cases from 157 studies published between 1990 and 2018...
2022: Respiration; International Review of Thoracic Diseases
https://read.qxmd.com/read/34446079/dietary-treatment-of-congenital-chylothorax-with-skimmed-breast-milk
#12
JOURNAL ARTICLE
Michaela Höck, Alexander Höller, Marlene Hammerl, Karina Wechselberger, Jakob Krösslhuber, Ursula Kiechl-Kohlendorfer, Sabine Scholl-Bürgi, Daniela Karall
BACKGROUND: Congenital chylothorax (CC) is a rare but potentially life-threatening condition in newborns. It is defined as an accumulation of chyle in the pleural cavity. The few publications regarding medical management and therapeutic dietary intervention motivated us to share our experience. METHODS: Neonates diagnosed with congenital chylothorax and treated at Innsbruck Medical University Hospital between 2013 and 2020 (n = 6, gestational age: 36 3/7, 32 5/7, 36 4/7, 35 0/7, 35 4/7, 37 3/7 weeks) were eligible for this report...
August 26, 2021: Italian Journal of Pediatrics
https://read.qxmd.com/read/33843702/the-use-of-high-dose-octreotide-in-management-of-neonatal-chylothorax-review
#13
REVIEW
M A Alhasoon
BACKGROUND: Being a rare condition, the incidence of chylothorax among neonates is low, but the mortality rate is high. In a dire effort to reduce the risk of death, octreotide treatment is used to effectively treat acquired and congenital chylothorax. Octreotide is proven to effectively treat chylothorax in pre-term and full-term neonates. However, previous studies have not consistently demonstrated the optimal dose of octreotide or the best mode of administration. The objectives of this work were to review previous literature to determine the outcomes of administering high doses of octreotide compared to lower dose regimens in neonates with chylothorax and to determine best practices...
2021: Journal of Neonatal-perinatal Medicine
https://read.qxmd.com/read/33494092/should-newborns-with-refractory-chylothorax-be-tried-on-higher-dose-of-octreotide
#14
Geza Vass, Ria Evans Fry, Charles C Roehr
Chylothorax is a rare but life-threatening condition in newborns, often requiring a prolonged hospital stay. To date, no unified guidance exists for best management approach. Octreotide, a somatostatin analogue, has been used to treat neonatal chylothorax due to its effect on the splanchnic circulation and lipid absorption. It is administered either subcutaneously or intravenously; for the latter, a dose range between 1 and 10 µg/kg/h is most commonly used. However, the optimal dose and way of administration remain unclear...
2021: Neonatology
https://read.qxmd.com/read/33294285/chylothorax-associated-with-congenital-complete-atrioventricular-block
#15
Shuhei Fujino, Hidehiko Maruyama, Keiko Tsukamoto, Hiroshi Ono, Tetsuya Isayama, Yushi Ito
Introduction  Congenital complete atrioventricular block (CCAVB) associated with congenital chylothorax is a rare finding that has been reported in only one case in the literature. We report here the case of an infant with CCAVB complicated by congenital chylothorax. Patient Report  We present the case of a male neonate with a birth weight of 2114 g. Fetal bradycardia and right pleural effusion were detected at gestational age of 22 weeks. Maternal serum levels of anti-Sjögren's-syndrome-related antigen A autoantibody were high (4840 U/mL)...
October 2020: American Journal of Perinatology Reports
https://read.qxmd.com/read/33209734/thoracoscopic-removal-of-a-displaced-thoracoamniotic-shunt-in-a-newborn-with-antenatal-pleural-effusion-a-case-report
#16
Goby T W Sham, Patrick H Y Chung, Iris M C Chan, W C Leung, Kenneth K Y Wong
Thoracoamniotic shunt has been considered as a treatment for antenatal pleural effusion and complication is rare. In majority of cases, the shunt can be removed uneventfully. In this article, we reported a rare complication of shunt migration resulting in the need of thoracoscopic removal at newborn period. The patient born at 39+3 weeks of gestation suffered from antenatal chylothorax detected at 28 weeks and was managed by intrauterine thoracoamniotic shunt insertion. This was complicated by shunt displacement, which caused respiratory distress after birth requiring ventilatory support and progressive pleural effusion in this patient...
October 2020: Translational Pediatrics
https://read.qxmd.com/read/32972739/thoracoscopic-repair-of-congenital-isolated-h-type-tracheoesophageal-fistula
#17
JOURNAL ARTICLE
Krystian Toczewski, Michal Rygl, Agata Dzielendziak, Barbora Frybova, Dariusz Patkowski
BACKGROUND/PURPOSE: The available literature on congenital isolated H-type tracheoesophageal fistula (TEF) is limited, and preferred approach varies among centers (cervicotomy, thoracotomy, thoracoscopy). We aimed to present one of the biggest case series of thoracoscopic approach for congenital isolated TEF and to assess the method's feasibility and outcomes. METHODS: Retrospective review of thoracoscopic TEF repair experiences at 2 European university pediatric surgery centers...
August 2021: Journal of Pediatric Surgery
https://read.qxmd.com/read/32618121/a-homozygous-variant-in-growth-and-differentiation-factor-2-gdf2-may-cause-lymphatic-dysplasia-with-hydrothorax-and-nonimmune-hydrops-fetalis
#18
Sietse M Aukema, Gerdien A Ten Brinke, Wim Timens, Yvonne J Vos, Ryan E Accord, Karianne E Kraft, Michiel J Santing, Leonard P Morssink, Esther Streefland, Cleo C van Diemen, Elianne Jle Vrijlandt, Christian V Hulzebos, Wilhelmina S Kerstjens-Frederikse
The etiology of nonimmune hydrops fetalis is extensive and includes genetic disorders. We describe a term-born female neonate with late onset extensive nonimmune hydrops, that is, polyhydramnios, edema, and congenital bilateral chylothorax. This newborn was successfully treated with repetitive thoracocentesis, total parenteral feeding, octreotide intravenously and finally surgical pleurodesis and corticosteroids. A genetic cause seemed plausible as the maternal history revealed a fatal nonimmune hydrops fetalis...
September 2020: American Journal of Medical Genetics. Part A
https://read.qxmd.com/read/32434361/povidone-iodine-chemical-pleurodesis-in-treating-spontaneous-chylothorax-in-pediatric-patients
#19
JOURNAL ARTICLE
Wei-Guang Long, Bin Cai, Yang Liu, Wen-Jie Wang
BACKGROUND: Chylothorax is a rare disease with a high mortality rate in pediatric patients like newborns and infants. As one of the minimally invasive treatments, chemical pleural pleurodesis has been gradually used in treating pediatric chylothorax patients in recent years. This study explored the feasibility, safety and effect of povidone-iodine chemical pleurodesis (CP) for spontaneous chylothorax in young pediatric patients. METHODS: From January 2009 to December 2019 the clinical data of 22 children treated for spontaneous chylothorax at Guangdong Second Provincial General Hospital were retrospectively analyzed...
May 2020: Annals of Palliative Medicine
https://read.qxmd.com/read/32051156/necrotising-enterocolitis-in-a-newborn-infant-treated-with-octreotide-for-chylous-effusion-is-octreotide-safe
#20
JOURNAL ARTICLE
Suresh Chandran, Arpan Agarwal, Genevieve Villablanca Llanora, Mei Chien Chua
Octreotide is a somatostatin analogue used for treating congenital chylothorax and congenital hyperinsulinism in infants. By increasing splanchnic arteriolar resistance and decreasing gastrointestinal blood flow, octreotide indirectly reduces lymphatic flow in chylous effusions.Splanchnic ischaemia following octreotide predisposes infants to necrotising enterocolitis (NEC). Although NEC occurrence in infants treated with octreotide for hyperinsulinaemic hypoglycaemia has been reported widely, its incidence in infants with chylothroax is low...
February 11, 2020: BMJ Case Reports
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