Mohammad H Fard-Aghaie, Georgios Makridis, Tim Reese, Bernd Feyerabend, Kim C Wagner, Andreas Schnitzbauer, Wolf O Bechstein, Felix Oldhafer, Moritz Kleine, Jürgen Klempnauer, Jens Rolinger, Silvio Nadalin, Alfred Königsrainer, Nikolaos Vassos, Robert Grützmann, Tamas Benkö, Andreas Paul, Jun Li, Lutz Fischer, Katharina Beaumont, Natascha Nüssler, René Fahrner, Utz Settmacher, Stefan Fichtner-Feigl, Wenzel Schöning, Johann Pratschke, Jennifer A Eckhoff, Roger Wahba, Christiane Bruns, Alexander Bernsmeier, Felix Braun, Thomas Becker, Georg Lurje, Ulf P Neumann, Jonas Dohmen, Steffen Manekeller, Jörg C Kalff, Arianeb Mehrabi, Markus W Büchler, Sven A Lang, Hans J Schlitt, Verena Tripke, Hauke Lang, Karl J Oldhafer
BACKGROUND: Caroli Disease (CD) and Caroli Syndrome (CS) are rare disorders presenting with dilation of the intrahepatic bile ducts. CD/CS are associated with cholangiocarcinoma (CCA). However, the true incidence of CCA is still unclear, although it may serve as an indication for surgery. In this paper, we analyzed (I) the incidence of CCA in German centers, (II) reviewed our single center population together with its clinical presentation and (III) performed a thorough literature review...
February 2022: HPB: the Official Journal of the International Hepato Pancreato Biliary Association