Nicola Fazio, Patrick Maisonneuve, Francesca Spada, Lorenzo Gervaso, Chiara Alessandra Cella, Marta Pozzari, Dario Zerini, Eleonora Pisa, Caterina Fumagalli, Massimo Barberis, Alice Laffi, Chiara Maria Grana C, Gianmarco Orsolini, Pierpaolo Prestianni, Guido Bonomo, Luigi Funicelli, Emilio Bertani, Paola Queirolo, Davide Ravizza, Manila Rubino, Giulio Tosti, Elisabetta Pennacchioli
Merkel cell carcinoma (MCC) is a very rare and aggressive neuroendocrine carcinoma originating from Merkel cells, typically with a skin nodule; however, it exceptionally presents with only a basin lymph node localization, with neither a cutaneous primary site nor distant metastases. From 1996 to 2020, among patients with histologically confirmed MCC managed at a neuroendocrine neoplasm-referral center, we selected those with an exclusive nodal basin, no distant metastasis, and an unknown primary site defined by cross-sectional and physical examination...
September 29, 2022: Cancers