Marta Delsoglio, Rebecca Capener, Anita MacDonald, Anne Daly, Catherine Ashmore, Sarah Donald, Lisa Gaff, Louise VanDorp, Rachel Skeath, Charlotte Ellerton, Camille Newby, Georgina Dunning, Clare Dale, Inderdip Hunjan, Lucy White, Heather Allen, Gary P Hubbard, Rebecca J Stratton
(1) Background: Poor palatability, large volume, and lack of variety of some liquid and powdered protein substitutes (PSs) for patients with phenylketonuria (PKU) and tyrosinemia (TYR) can result in poor adherence. This study aimed to evaluate a new unflavoured, powdered GMP-based PS designed to be mixed into drinks, foods, or with other PSs, in patients with PKU and TYR. (2) Methods: Paediatric and adult community-based patients were recruited from eight metabolic centres and prescribed ≥1 sachet/day (10 g protein equivalent (PE)) of the Mix-In-style PS over 28 days...
August 17, 2023: Nutrients