Whitney J Tang, Bo Gu, Samuel Montalvo, Sally Dunaway Young, Dana M Parker, Constance de Monts, Paxton Ataide, Noirin Ni Ghiollagain, Matthew T Wheeler, Carolina Tesi Rocha, Jeffrey W Christle, Zihuai He, John W Day, Tina Duong
Assessing endurance in non-ambulatory individuals with Spinal Muscular Atrophy (SMA) has been challenging due to limited evaluation tools. The Assisted 6-Minute Cycling Test (A6MCT) is an upper limb ergometer assessment used in other neurologic disorders to measure endurance. To study the performance of the A6MCT in the non-ambulatory SMA population, prospective data was collected on 38 individuals with SMA (13 sitters; 25 non-sitters), aged 5 to 74 years (mean = 30.3; SD = 14.1). The clinical measures used were A6MCT, Revised Upper Limb Module (RULM), Adapted Test of Neuromuscular Disorders (ATEND), and Egen Klassifikation Scale 2 (EK2)...
December 8, 2023: Journal of Clinical Medicine