Nico De Paola, Santina Ermito, Antonella Nahom, Angela Dinatale, Elisa Maria Pappalardo, Sabina Carrara, Alessandro Cavaliere, Cristiana Brizzi
OBJECTIVE: Left isomerism, also called polysplenia, is a laterality disturbance associated with with paired leftsidedness viscera and multiple small spleens. Left isomerism, heart congenital abnormalities and gastrointestinal malformation are strongly associated. METHODS: We present a case of prenatal diagnosis of left isomerism in a fetus with a structurally normal heart. CONCLUSION: Left isomerism syndrone may coesist with a structurally normal heart...
July 2009: Journal of Prenatal Medicine