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Hollow visceral myopathy

H J Williams, N Reading, S Rabbani, J G Lanham
No abstract text is available yet for this article.
March 2014: British Journal of Hospital Medicine
Robert J Huang, Chohee Yun, Linda Nguyen
No abstract text is available yet for this article.
October 2013: Digestive and Liver Disease
C Van Rensburg, S W Moore, M Zaahl
African degenerative leiomyopathy (ADL, DL, Bantu pseudo-Hirschsprung's disease) is a distinctive visceral myopathy, of unknown etiology, occurring in Africa. It has a classical clinical and histologic picture in young indigenous African children. It presents as intestinal pseudo-obstruction with a massive megacolon due to degeneration of smooth muscle without aganglionosis. Because of its late presentation and geographical and ethnic distribution, it is thought to be an acquired degenerative hollow visceral myopathy...
December 2012: Pediatric Surgery International
S H T Zaidi, M Arif, Z Zaidi
No abstract text is available yet for this article.
February 2003: JPMA. the Journal of the Pakistan Medical Association
J Villarreal, M Sood, T Zangen, A Flores, R Michel, N Reddy, C Di Lorenzo, P E Hyman
BACKGROUND: Colonic manometry helps discriminate functional and behavioral causes for childhood constipation from colonic neuromuscular disease. METHODS: Of 375 colonic manometries performed for clinical indications, 12 could not be interpreted because of chronic colonic dilation. Based on colonic manometries that showed either no contractions or an absence of the gastrocolonic response or an absence of high-amplitude propagating contractions, the authors recommended diverting colostomies or ileostomies in 12 chronically constipated children (mean age, 4 years; range, 2-14 years, 5 boys)...
November 2001: Journal of Pediatric Gastroenterology and Nutrition
M Arslan, Y Bayraktar, G Oksuzoglu, A Ozdemir, C Sokmensuer, M C Yagmurdur, A R Soylu, B Uzunalimoglu, B Kayhan
BACKGROUND/AIMS: Chronic intestinal pseudo-obstruction is a rare clinical syndrome characterized by symptoms and signs of intestinal obstruction without any organic lesion obstructing the intestine. Visceral myopathy is one of the etiological causes and full thickness intestinal biopsy is essential for reaching a diagnosis. In this article we describe 4 cases of hollow visceral myopathy; our aim is to stress the importance of full thickness biopsy. METHODOLOGY: Four cases of hollow visceral myopathy are studied herein...
January 1999: Hepato-gastroenterology
R Ghavamian, D T Wilcox, P G Duffy, P J Milla
PURPOSE: Hollow visceral myopathy is a rare clinical entity characterized by impaired intestinal function in the absence of mechanical occlusion. It can affect the smooth muscle of the whole or segments of the gastrointestinal tract and occasionally the urinary tract. We examined the urological manifestations of hollow visceral myopathy and management in the pediatric population. MATERIALS AND METHODS: We reviewed the records of 14 male patients 1 day to 2 years old (mean age 4...
September 1997: Journal of Urology
J E Martin, M Benson, M Swash, V Salih, A Gray
A patient with hollow visceral myopathy is reported in whom light microscopical studies of the small and large intestine showed typical features of degeneration, thinning, and fibrous replacement of smooth muscle of the gastrointestinal tract. Electron microscopy showed a striking increase in collagen with minimal fibroblast proliferation. Smooth muscle fibres had a range of ultrastructural abnormalities including myofilament disarray, electron lucency of the cytoplasm, and proliferation of the endoplasmic reticulum...
July 1993: Gut
C Di Lorenzo, A F Flores, S N Reddy, W J Snape, G Bazzocchi, P E Hyman
Pressure changes were evaluated in the transverse, descending, and rectosigmoid colon of 30 children with chronic intestinal pseudo-obstruction. Twenty two had severe lifelong constipation and eight had symptoms suggesting a motility disorder exclusively of the upper gastrointestinal tract. Based on prior antroduodenal manometry, 24 children were diagnosed as having a neuropathic and six a myopathic form of intestinal pseudo-obstruction. On the day of study, endoscopy was used to place a manometry catheter into the transverse colon and intraluminal pressure was recorded for more than four hours...
June 1993: Gut
J R Mathias, M H Clench
Gastrointestinal motor dysfunction, intestinal pseudo-obstruction syndromes, and hollow visceral neuropathy and myopathy were previously considered functional bowel diseases but are now recognized to be organic disorders. They may alter the muscle of the intestinal wall or the nerves of the myenteric plexus, or both. Their symptoms of chronic unexplained abdominal pain, abdominal distention and bloating, early satiety, nausea, vomiting, and alternating diarrhea and constipation are the most common and perhaps the most difficult problems encountered by gastroenterologists...
March 1995: Postgraduate Medicine
J A Smith, S C Hauser, J L Madara
A patient is described who had unexplained, vague abdominal pain for 7 years and subsequently presented with worsening pain and mild dilatation of the distal small intestine. Gross examination of a resected ileal segment demonstrated thinning of the muscularis propria. Light- and electron-microscopic examination revealed a myopathy which preferentially involved the external longitudinal layer of the muscularis propria and was characterized by vacuolar degeneration of smooth muscle cells. No inflammatory infiltrate or neural or vascular lesions were present...
April 1982: American Journal of Surgical Pathology
M D Schuffler, C A Rohrmann, R G Chaffee, D L Brand, J H Delaney, J H Young
Twenty-seven cases of chronic intestinal pseudo-obstruction are reported. The causes of pseudo-obstruction were progressive systemic sclerosis in 14, hollow visceral myopathy in 4, visceral neuropathy in 2, sclerosing mesenteritis in 1, and jejunal diverticulosis in 1. No identifiable cause was found in five. Chronic pseudo-obstruction is a long-term illness characterized by vomiting, abdominal distention, abdominal pain and weight loss. Involvement is often present throughout the intestine so that patients may present with a variety of symptoms deriving from the esophagus, stomach, small intestine, and colon...
May 1981: Medicine (Baltimore)
C Nezelof, E Vivien, P Bigel, C Nihoul-Fekete, F Arnaud-Battandier, J L Bresson, P Arhan, C Ricour
The case reported concerns a child with chronic intestinal pseudo-obstruction (CIPO) whose digestive manifestations (intestinal adynamia and distension) were present from the age of 6 months and lasted, despite medical and surgical treatments until 4 years of age, when death occurred. The multiple samplings showed important inflammatory reactions centred on the muscular layers of the small intestine, together with degenerative lesions of the muscular fibres, progressively leading to fibrosis and atrophy of the intestinal wall with secondary and final impairment of the myenteric plexuses...
December 1985: Archives Françaises de Pédiatrie
C Isaacson, H C Wainwright, D G Hamilton, L Ou Tim
Familial (hereditary) hollow visceral myopathy is a rare cause of chronic intestinal pseudo-obstruction. Fourteen black patients with the disease, 6 males and 8 females, are described. The earliest morphological lesion is an isolated smooth-muscle degeneration of the muscularis propria of the bowel, especially the colon. The pathological changes are lysis and disappearance of the muscularis propria of the bowel wall, leading to dilatation and intra-luminal stasis. progressive involvement results in large areas of defective muscularis propria...
June 22, 1985: South African Medical Journal, Suid-Afrikaanse Tydskrif Vir Geneeskunde
M E Ament, J Vargas
Chronic intestinal pseudo-obstruction is a rare disorder characterized by ineffective intestinal propulsion in the absence of mechanical factors. It depends on isolated or associated disturbances of intrinsic and extrinsic innervation of the smooth muscle, neurotransmitters and hormones. In children the most common causes are postoperative paralytic ileus, pneumonia or pancreatitis, occurring usually in the first year of life. There is also hereditary transmission, comprising the familial visceral myopathy (hollow visceral myopathy) and the familial visceral neuropathy...
July 1988: Arquivos de Gastroenterologia
C A Rodrigues, N A Shepherd, J E Lennard-Jones, P R Hawley, H H Thompson
A family with at least six members affected by hollow organ visceral myopathy is described. Patients in the first or second decades of life developed symptoms which included weight loss, nausea and vomiting, abdominal pain and distension, constipation and diarrhoea, and urinary symptoms. The radiological features of the disease consisted of oesophageal aperistalsis, megaduodenum, and variable dilatation of the small and large bowel. Four patients had urinary tract involvement with dilatation of the ureters and/or incomplete bladder emptying...
September 1989: Gut
P I Mansell, R B Tattersall, M Balsitis, J Lowe, R C Spiller
A 29 year old man with a history of childhood polymyositis developed insulin dependent diabetes and was found coincidentally to have chronic intestinal pseudo-obstruction due to visceral myopathy. Multiple full thickness biopsy specimens showed severe disease in the duodenum and the proximal jejunum only, with less involvement distally. Total parenteral nutrition has been avoided for more than a year by enteral feeding through a fine bore jejunostomy catheter positioned with its tip in the distal jejunum.
March 1991: Gut
C Di Lorenzo, A F Flores, S N Reddy, P E Hyman
We evaluated colon manometry as a means of differentiating causes of intractable constipation in children. We studied pressure changes in the transverse, descending, and rectosigmoid colons of 23 children with intractable constipation. All patients had a history of less than one bowel movement per week for longer than 2 years without resolution after conventional medical management. The possibility of Hirschsprung disease was excluded in all. On the basis of pathologic and manometric studies of the upper gastrointestinal tract, 10 patients had a diagnosis of gastrointestinal neuropathy and two had a diagnosis of myopathy...
May 1992: Journal of Pediatrics
D Higman, P Peters, M Stewart
A family with hereditary hollow visceral myopathy is described, with characteristic variation in expression between affected members. Very severe and widespread involvement of the gastrointestinal and urinary tracts in 1 patient contrasted with isolated urinary tract involvement in 2 others, and it is suggested that hollow visceral myopathy should be considered in the differential diagnosis of primary detrusor failure. The management of urinary tract involvement is discussed and a conservative approach is recommended...
October 1992: British Journal of Urology
M D Schuffler, C E Pope
Twelve relatives of a 15-year-old girl with idiopathic intestinal pseudoobstruction were studied with esophageal manometry or cine-esophagography to determine whether the disease was genetically transmitted. Four maternal relatives, including the patient's mother, 13-year-old brother, one aunt, and one of that aunt's children had mild dysphagia and esophageal motor dysfunction. In addition, the patient's mother and 13-year-old brother had a flaccid bladder and bilateral ureteral reflux, respectively. The brother had abnormal bladder smooth muscle by light microscopy...
August 1977: Gastroenterology
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