Read by QxMD icon Read

Aural atresia

Elisa Tassano, Mariasavina Severino, Silvia Rosina, Riccardo Papa, Domenico Tortora, Giorgio Gimelli, Cristina Cuoco, Paolo Picco
BACKGROUND: Deletions of the long arm of chromosome 18 cause a common autosomal syndrome clinically characterized by a protean clinical phenotype. CASE PRESENTATION: We report on a 16-month-old male infant affected by fever attacks apparently unrelated with any infectious or inflammatory symptoms, growth retardation, bilateral vertical talus, congenital aural atresia, dysmorphisms, mild psychomotor delay, and peculiar neuroradiological features. Array-CGH analysis revealed one of the smallest 18q22...
2016: Molecular Cytogenetics
M Leinung, E Zaretsky, B P Ernst, B Trier, T Stöver, C Hey
No abstract text is available yet for this article.
October 11, 2016: Laryngo- Rhino- Otologie
Randall A Bly, Amit D Bhrany, Craig S Murakami, Kathleen C Y Sie
Microtia reconstruction is a challenging endeavor that has seen significant technique evolution. It is important to educate patients and their families to determine the best hearing rehabilitation and ear reconstructive options. Microtia is often associated with aural atresia, hearing loss, and craniofacial syndromes. Optimal care is provided by multiple disciplines, including a reconstructive surgeon, an otologic surgeon, an audiologist, and a craniofacial pediatrician. Microtia management includes observation, prosthetic ear, autologous cartilage reconstruction, or alloplastic implant placement...
November 2016: Facial Plastic Surgery Clinics of North America
Hong Chan Kim, Chul Ho Jang, Chung Man Sung, Eun Kyung Jung, Yong Beom Cho
No abstract text is available yet for this article.
September 12, 2016: Brazilian Journal of Otorhinolaryngology
Vânia Henriques, Rafaela Teles, Ana Sousa, Roberto Estevão, Jorge Rodrigues, Alexandra Gomes, Francisco Silva, Ângelo Fernandes, Fausto Fernandes
Congenital middle ear malformations are rare. Most part of them are usually associated with other malformations, such as aural atresia, microtia, and dysmorphic craniofacial features. A clinical case of a 24-year-old male with a right-sided conductive hearing loss since his childhood, without craniofacial malformation, is presented. He was proposed for exploratory tympanotomy under the suspicious diagnosis of otosclerosis. The surgery revealed an abnormal location of stapes' superstructure, which was attached to the promontory and had an isolated and mobile osseous footplate in the oval window...
2016: Case Reports in Otolaryngology
Shane Zim, Janet Lee, Brian Rubinstein, Craig Senders
OBJECTIVE:   The objective of this study was to determine whether patients with isolated microtia or aural atresia have an increased prevalence of renal or cervical vertebral anomalies. DESIGN:   The study design was a retrospective medical record review. SETTING:   The setting was the following four distinct institutions: an urban tertiary care children's hospital, two urban academic medical centers, and a staff-model health maintenance organization...
September 15, 2016: Cleft Palate-craniofacial Journal
Robert Reed, Matthew Hubbard, Bradley W Kesser
OBJECTIVES: To compare speech/language development and academic progress between children with right versus left congenital aural atresia (CAA). STUDY DESIGN: Case control survey and review of audiometric data. SETTING: Tertiary care academic practice. PATIENTS: Children with unilateral CAA. MAIN OUTCOME MEASURES: Demographic and audiometric data; rates of grade retention, use of any hearing or learning resource, and behavioral problems...
September 14, 2016: Otology & Neurotology
M Leinung, Y Zaretsky, B Ernst, B Vaerst, T Stöver, C Hey
BACKGROUND: The audiological treatment of children with aural atresia makes high demands on physicians and acousticians. Conventional hearing systems are often not tolerated by children and therefore do not meet the needs of the early and efficient therapy of hearing disorders. Aim of the present study was the evaluation of the audiological functional gain in children with uni- and bilateral aural atresia provided with the middle ear implant Vibrant Soundbridge(®) (VSB(®)) below the age of 6 years as well as the analysis of parents' satisfaction assessed with questionnaires...
September 2016: Laryngo- Rhino- Otologie
M Leinung, E Zaretsky, B P Lange, V Hoffmann, T Stöver, C Hey
The aim of this pilot study was to determine the acceptance and benefit from the middle ear implant system Vibrant Soundbridge(®) (VSB, MED-EL Corporation, Austria) by means of a questionnaire, compared to a previously used conventional bone conducting hearing device, in preschool children with unilateral congenital aural atresia. Prospective cohort study. All nine children with unilateral congenital aural atresia used the VSB and had previous experience with a bone conducting hearing device. The benefit from the VSB was evaluated by questionnaires concerning acceptance of hearing aids, handling, listening effort, behavior, quality of life, and the duration of daily use and compared to the experience with the bone conducting hearing device...
August 25, 2016: European Archives of Oto-rhino-laryngology
Hetal Marfatia, Ratna Priya, Nilam U Sathe, Shampa Mishra
Baha has proven performance and advantages for patients with aural atresia or chronic ear drainage. Being a per cutaneous osseo integrated implant the skin around the fixture is in contact with a foreign body that leads to chronic inflammatory reaction and complications such as skin irritation and overgrowth occur frequently. Challenges that are faced during Baha surgery include those during candidate selection, work up, anesthesia related as well as intra-operative and post operative complications. Ours was a retrospective and observational study where case records of 10 patients who underwent Baha surgery in the Department of E...
September 2016: Indian Journal of Otolaryngology and Head and Neck Surgery
Danni Wang, Shouqin Zhao, Qingguo Zhang, Yi Li, Xiaobo Ma, Ran Ren
OBJECTIVES: To report an integrating surgical method of Vibrant SoundBridge (VSB) implant and auricle reconstruction. METHODS: 4 cases of congenital bilateral external/middle ear malformation were enrolled. All of them were diagnosed as bilateral bony atresia and grade III microtia. Stapes vibroplasty was performed for all subjects in one operation with auricle reconstruction stage 3. The clinical information and hearing outcomes were analyzed. RESULTS: Satisfied aesthetic outcomes were confirmed by sculptured outline and symmetric shape on both sides...
July 2016: International Journal of Pediatric Otorhinolaryngology
Ritu Verma, Manisha Jana, Ashu Seith Bhalla, Arvind Kumar, Rakesh Kumar
Aural atresia is a rare congenital malformation of the external and middle ear. There are several syndromic associations of this anomaly with those involving the first and second branchial arches. Occurrence of aural atresia with sclerosing skeletal dysplasia is unknown and has never been reported. The co-existence of a sclerosing dysplasia can make the surgical treatment in aural atresia difficult and risky; and the auditory improvement may not be as expected. Moreover, internal auditory canal narrowing and hence sensorineural hearing loss in sclerosing dysplasia might add to the already existing conductive hearing loss in such patients...
May 8, 2016: World Journal of Clinical Pediatrics
Keguang Chen, Dongming Yin, Huiying Lyu, Lin Yang, Tianyu Zhang, Peidong Dai
CONCLUSIONS: With the aggravation of the external auditory canal malformation, the size of extra-niche fossa became smaller, providing concrete data and valuable information for the better design, selecting and safer implantation of the transducer in the area of round window niche. Three-dimensional measurements and assessments before surgery might be helpful for a safer surgical approach and implantation of a vibrant soundbridge. OBJECTIVES: The aim of this study was to investigate whether differences exist in the morphology of the posterior tympanum related to the round window vibroplasty among congenital aural atresia (CAA), congenital aural stenosis (CAS), and a normal control group, and to analyze its effect on the round window implantation of vibrant soundbridge...
2016: Acta Oto-laryngologica
Kimitaka Kaga, Hirotaka Asato
CONCLUSION: In patients with unilateral microtia and atresia after reconstruction of the auricle and external canal and fitting of a canal-type hearing aid for the operated ear, the ability to discriminate the inter-aural intensity difference (IID) was acquired in all of the patients, whereas that to discriminate inter-aural time difference (ITD) was acquired in one-half of the patients. OBJECTIVE: To study the post-operative sound lateralization ability in patients with unilateral microtia and atresia after reconstruction surgery of the auricle and external canal and fitting of a canal-type hearing aid of the operated ear...
2016: Acta Oto-laryngologica
Kun Chen, Chenyan Jiang, Qingwei Wu, Yiyuan Sun, Runjie Shi
Atresiaplasty is still a challenge for otolaryngologist, although the operation technique has been modified several times over the past decades. This study describes a reliable flap technique for combining atresiaplasty with total auricular reconstruction by performing the total auricular reconstruction with the MEDPOR framework at the same time as the atresiaplasty for patients with microtia and congenital aural atresia. We performed a prospective study of the medical records of 18 consecutive patients with congenital aural atresia...
December 2015: Indian Journal of Surgery
Joong-Wook Shin, Sung Huhn Kim, Jae Young Choi, Hong-Joon Park, Seung-Chul Lee, Jee-Sun Choi, Han Q Park, Ho-Ki Lee
OBJECTIVES: Bone-anchored hearing aids (BAHA) occasionally cause soft tissue problems due to abutment. Because Sophono does not have abutment penetrating skin, it is thought that Sophono has no soft tissue problem relating to abutment. On the other hand, transcutaneous device's output is reported to be 10 to 15 dB lower than percutaneous device. Therefore, in this study, Sophono and BAHA were compared to each other from surgical and audiological points of view. METHODS: We retrospectively reviewed the medical records of 9 Sophono patients and 10 BAHA patients...
March 2016: Clinical and Experimental Otorhinolaryngology
Katsumi Doi, Sho Kanzaki, Kozo Kumakawa, Shin-ichi Usami, Satoshi Iwasaki, Noboru Yamanaka, Yasushi Naito, Kiyofumi Gyo, Tetsuya Tono, Haruo Takahashi, Yukihiko Kanda
Middle ear implants (MEIs) such as the Vibrant Soundbridge (VSB) are attractive and alternative treatments for patients with conductive, sensorineural, and mixed hearing loss who do not benefit from, or who choose not to wear, conventional hearing aids (HAs). Recent studies suggest that MEIs can provide better improvements in functional gain, speech perception, and quality of life than HAs, although there are certain risks associated with the surgery which should be taken into consideration, including facial nerve or chorda tympanic nerve damage, dysfunctions of the middle and inner ears, and future device failure/explantation...
December 2015: Nihon Jibiinkoka Gakkai Kaiho
Bradley W Kesser, Erika D Cole, Lincoln C Gray
OBJECTIVE: To investigate the emergence of binaural summation in patients with unilateral congenital aural atresia undergoing surgical correction. STUDY DESIGN: Preoperative and postoperative audiometric testing in a prospective cohort of 10 patients with unilateral congenital aural atresia. SETTING: University-based tertiary care center. PATIENTS: Ten patients (ages 6-53) with an average 69 dB (±9 dB sd) unilateral conductive hearing loss, normal hearing in the nonatretic ear, and normal bone conduction in the atretic ear...
June 2016: Otology & Neurotology
Y Si, Y Liu, Q H Huang, M J Liang, H L Jiang, G Xu, Z G Zhang
OBJECTIVE: To investigate the clinical application of scalp skin grafts in reconstruction of external auditory meatus in congenital aural atresia. METHODS: We conducted a retrospective study on 85 patients of congenital aural atresia, all of whom were unilateral, operated from March of 2008 to December of 2010 in ENT department of the Sun Yat-Sen Memorial Hospital. The patients enrolled in the study were between 6 to 37 years old (median age 12 years), 55 male and 30 female...
February 2016: Zhonghua Er Bi Yan Hou Tou Jing Wai Ke za Zhi, Chinese Journal of Otorhinolaryngology Head and Neck Surgery
Matthew G Crowson, Debara L Tucci
An osseointegrated implant (e.g. bone-anchored hearing aid, BAHA) is a surgically implantable device for unilateral sensorineural and unilateral or bilateral conductive hearing loss in patients who otherwise cannot use or do not prefer a conventional air conduction hearing aid (ACHA). The specific indications for an osseointegrated implant are evolving and dependent upon the country or regulatory body overseeing the provision of these devices. However, there are general groups of patients who would be likely to benefit, one such group being patients with congenital aural atresia...
2016: Audiology & Neuro-otology
Fetch more papers »
Fetching more papers... Fetching...
Read by QxMD. Sign in or create an account to discover new knowledge that matter to you.
Remove bar
Read by QxMD icon Read

Search Tips

Use Boolean operators: AND/OR

diabetic AND foot
diabetes OR diabetic

Exclude a word using the 'minus' sign

Virchow -triad

Use Parentheses

water AND (cup OR glass)

Add an asterisk (*) at end of a word to include word stems

Neuro* will search for Neurology, Neuroscientist, Neurological, and so on

Use quotes to search for an exact phrase

"primary prevention of cancer"
(heart or cardiac or cardio*) AND arrest -"American Heart Association"