João Fernandes-Serodio, Sergio Prieto-González, Georgina Espígol-Frigolé, Roberto Ríos-Garcés, Verónica Gómez-Caverzaschi, Olga Araújo, Gerard Espinosa, Raül Jordà-Sánchez, Marco A Alba, Luis Quintana, Miquel Blasco, Elena Guillen, Odette Viñas, Estíbaliz Ruiz-Ortiz, Laura Pelegrín, Maite Sainz de la Maza, Bernardo Sánchez-Dalmau, Adriana García-Herrera, Manel Solé, Paola Castillo, Iban Aldecoa, María D Cano, Jacobo Sellarés, Fernanda Hernández-González, Carlos Agustí, Carmen M Lucena, Antonio López-Rueda, Marcelo Sánchez, Mariana Benegas, Sebastián Capurro, Raimon Sanmartí, Josep M Grau, Isabel Vilaseca, Isam Alobid, Maria C Cid, José Hernández-Rodríguez
BACKGROUND: Microscopic polyangiitis (MPA) and granulomatosis with polyangiitis (GPA) are the two major antineutrophil cytoplasmic antibody (ANCA)-associated vasculitis (AAV). OBJECTIVES: To characterize a homogenous AAV cohort and to assess the impact of clinicopathological profiles and ANCA serotypes on clinical presentation and prognosis. Clinical differences in GPA patients according to ANCA serotype and the diagnostic yield for vasculitis of biopsies in different territories were also investigated...
March 11, 2024: Journal of Internal Medicine