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Rosai dorfman

Carolina Martínez-Ciarpaglini, Carlos Monteagudo
No abstract text is available yet for this article.
November 23, 2016: American Journal of Dermatopathology
Fandresena Arilala Sendrasoa, Irina Mamisoa Ranaivo, Onivola Raharolahy, Malalaniaina Andrianarison, Naina Harinjara Razanakoto, Lala Soavina Ramarozatovo, Fahafahantsoa Rapelanoro Rabenja
Rosai-Dorfman disease is a rare, benign histiocytic proliferative disorder that usually affects the lymph nodes. Although extranodal involvement has been reported in diverse sites, manifestation in the cardiovascular system is extremely rare. Specifically, cardiac involvement in Rosai-Dorfman disease is an extraordinarily infrequent event. We describe a case of a 36-year-old female who presented Rosai-Dorfman disease of multiple organs including the heart, with poor prognosis.
2016: Case Reports in Medicine
C F Classen, M Minkov, T Lehrnbecher
Rare histiocytoses, also called non-Langerhans cell histiocytoses, include all proliferative disorders of histiocytes, macrophages and dendritic cells that are not classified as Langerhans cell histiocytosis (LCH) and do not belong to the hemophagocytic lymphohistiocytosis (HLH) group of diseases. Thus, the term includes numerous benign or malignant, localized or systemic, adult or pediatric diseases. The classification of the histiocytic disorders has been revised several times. Here, we follow the classification recently published by Jean Francois Emile and an international expert panel, defining subgroups of histiocytoses described as L-Group, C-Group, M-Group, R-Group, and H-Group, which stands for LCH-like, cutaneous or mucocutaneous, malignant, Rosai-Dorfman-Disease like and HLH like...
November 2016: Klinische Pädiatrie
Yi Xie, Stefania Pittaluga, Susan Price, Mark Raffeld, Jamie Hahn, Elaine S Jaffe, V Koneti Rao, Irina Maric
Autoimmune lymphoproliferative syndrome is rare genetic disorder characterized by defective FAS-mediated apoptosis, autoimmune disease, accumulation of mature T-cell receptor alpha/beta positive, CD4 and CD8 double-negative T cells and increased risk for lymphoma. Despite frequent hematological abnormalities, literature is scarce regarding the bone marrow pathology in autoimmune lymphoproliferative syndrome. We retrospectively reviewed 3l bone marrow biopsies from a cohort of 240 patients with germline FAS mutation...
October 20, 2016: Haematologica
Ana Gameiro, Miguel Gouveia, José Carlos Cardoso, Oscar Tellechea
Rosai-Dorfman disease is a benign histiocytic proliferative disorder of unknown etiology. The disease mainly affects lymph node tissue, although it is rarely confined to the skin. Here, we describe a 53-year-old woman with purely cutaneous Rosai-Dorfman disease. The patient presented with a large pigmented plaque on her left leg, and sparse erythematous papules on her face and arms. A complete clinical response was achieved with thalidomide, followed by recurrence at the initial site one year later. The histological examination displayed the typical features of Rosai-Dorfman disease in the recent lesions but not in the older lesions...
September 2016: Anais Brasileiros de Dermatologia
Philip Kin-Wai Wong, Daniel J Lee, Saul Harari, Bruce J Barron
Langerhan's histiocytosis is a not uncommon disease, but a related disorder, Rosai-Dorfman (RDD) with extensive or exclusive extranodal distribution, is relatively rare. Ga and PET/CT imaging have typically been used for diagnosis and tracking response to treatment. The authors present a very unusual case wherein lesions of RDD actively accumulated Tc-sestamibi, which was injected as part of a scan to localize a parathyroid adenoma.
December 2016: Clinical Nuclear Medicine
C Shi, H W Guan, Q P Zhang, Z Y Hua, W J Qi, L Z Zhang
No abstract text is available yet for this article.
November 8, 2016: Zhonghua Bing Li Xue za Zhi Chinese Journal of Pathology
Han Chen, Haiyan Zhou, Zhi Song
No abstract text is available yet for this article.
December 2016: Neurology® Neuroimmunology & Neuroinflammation
Jonathan C Baker, Michael Kyriakos, Douglas J McDonald, David A Rubin
We report a 19-year-old man with the rare occurrence of primary osseous Rosai-Dorfman disease (RDD). The patient presented with a painful, solitary, bone marrow-replacing lesion in the distal femur. A diagnosis of chronic osteomyelitis was initially made on tissue from a CT-guided needle biopsy of the lesion; however, the diagnosis of RDD was eventually made after histological and immunohistochemical analysis of material from a subsequent curettage. No lymphadenopathy or other sites of involvement were found on clinical evaluation and PET-CT...
October 26, 2016: Skeletal Radiology
Bruno Niemeyer de Freitas Ribeiro, Edson Marchiori
No abstract text is available yet for this article.
July 2016: Radiologia Brasileira
Sathiyamoorthy Selvarajan, Lee Ming
No abstract text is available yet for this article.
February 2016: Pathology
Amir Maghsoudi, Jane Nankervis
No abstract text is available yet for this article.
February 2016: Pathology
B N Mahanta, T Goswami Mahanta
A young male presented with recurrent neck swellings with initial leucocyte count of 16800/mm3, with non-caseating glands on ultrasonography neck. FNAC showed mixed cellularity with histiocytic and marked lymphophagocytosis as seen in Rosai Dorfman Disease. Immunohistochemistry demonstrated CD 25, Ki 67 and CD 68 in histiocytes. Her responded to supportive treatment alone.
October 2016: Journal of the Association of Physicians of India
Matthew Raymond Summers, Gosta Pettersson, Joseph F Maalouf, Wael A Jaber
No abstract text is available yet for this article.
October 14, 2016: European Heart Journal
Harshit Jain, Nikhil Gupta, Jalees Fatima, Ritu Karoli, Vaibhav Shukla
No abstract text is available yet for this article.
January 2016: Journal of the Association of Physicians of India
Marta Drake-Pérez, James G Smirniotopoulos
This article reviews the most frequent extra-axial tumors of the central nervous system, from the most common meningioma to some uncommon conditions, like Rosai-Dorfman disease, focusing on imaging techniques, pearls, and pitfalls as well as a more practical approach.
November 2016: Neuroimaging Clinics of North America
Edward Chen, Peter Pavlidakey, Naveed Sami
No abstract text is available yet for this article.
September 2016: JAAD Case Reports
Jay Karajgikar, Gregory Grimaldi, Barak Friedman, John Hines
Rosai-Dorfman disease is a rare disorder of unknown etiology caused by the proliferation of histiocytes within lymph nodes, predominantly in the cervical chain. Extranodal sites may be involved as well, with involvement of nearly every organ system described in the literature. Abdominal and pelvic manifestations of Rosai-Dorfman disease are extremely rare. We present four cases of abdominal and pelvic involvement by Rosai-Dorfman disease, specifically within the biliary tract, pancreas, spleen, and presacral space...
September 13, 2016: Clinical Imaging
Zhengxiang Luo, Yansong Zhang, Penglai Zhao, Hucheng Lu, Kun Yang, Yuhai Zhang, Yanjun Zeng
OBJECTIVES: The study aimed to summarize the clinical characteristics of Rosai-Dorfman syndrome primarily involved in central nervous system and to explore diagnosis and treatment. METHODS: By combining literature review in with our study, we analyzed the clinical, imaging and pathological characteristics as well as treatment and prognosis for three cases of Rosai-Dorfman syndrome primarily involved in the central nervous system. RESULTS: The largest of multiple intracranial lesions was totally resected, and steroid administration and radiotherapy were performed in phases for the remaining lesions...
September 28, 2016: World Neurosurgery
Abid Hussain, Ashwani Tandon, Aruna K Prayaga, Tara Roshni Paul, Anukonda M V R Narendra
OBJECTIVES: Rosai-Dorfman disease (RDD) is an uncommon, benign histiocytic disorder of unknown etiology, typically presenting in young adulthood. We highlight the cytomorphology of RDD and correlate it with the histopathology. STUDY DESIGN: All cases diagnosed as RDD on fine-needle aspiration cytology between January 2001 and June 2015 were included. Clinical details were obtained from medical records. The cytology smears were reviewed along with the histopathology and immunohistochemistry, wherever available...
September 28, 2016: Acta Cytologica
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