Barbara Pieklarz, Ewa Gińdzieńska-Sieśkiewicz, Izabela Zawadzka, Magdalena Bagrowska, Joanna Daniluk, Joanna Konopińska, Otylia Kowal-Bielecka, Diana Anna Dmuchowska
Purtscher-like retinopathy (PLR) is an uncommon occlusive microangiopathy associated with various systemic conditions. We report a case of PLR related to severe progressive systemic sclerosis (SSc), an autoimmune disease characterized by widespread angiopathy and fibrosis, in a 44-year-old Caucasian male diagnosed with early diffuse cutaneous systemic sclerosis (dSSc). Upon ophthalmological examination, pathognomonic fundoscopy abnormalities were found. Spectral domain optical coherence tomography (SD-OCT), angio-OCT, and visual field results are documented at initial diagnosis and follow-up visits...
March 10, 2023: Biomedicines