Domitilla Russo, Francesco Cappelli, Gianluca Di Bella, Giacomo Tini, Aldostefano Porcari, Alberto Cipriani, Marco Canepa, Marco Merlo, Roberto Licordari, Pier Filippo Vianello, Mattia Zampieri, Laura De Michieli, Riccardo Scirpa, Federico Perfetto, Gianfranco Sinagra, Camillo Autore, Claudio Rapezzi, Maria Beatrice Musumeci
BACKGORUND: Hereditary transthyretin(vATTR) cardiac amyloidosis has extremely different features according to the type of transthyretin(TTR) mutation. Data about electrocardiographic findings(ECG) in vATTR are limited and not informative of genotype correlation. Aim of this study is to analyze ECG characteristics and their correlation to clinical and echocardiographic aspects in patients with vATTR, focusing on different TTR mutations. METHODS AND RESULTS: This is a multicentric, retrospective, observational study performed in six Italian referral centres...
September 9, 2023: International Journal of Cardiology