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Moyamoya disease

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https://www.readbyqxmd.com/read/29449517/-a-case-of-moyamoya-disease-with-postoperative-cerebral-hyperperfusion-syndrome-followed-by-cerebral-infarction-due-to-watershed-shift
#1
Kimitoshi Sato, Shun Tsudaka, Takanori Miki, Norikata Kobayashi, Taro Yamashita, Kiyoharu Imataka, Takashi Yoshida, Fuminori Shimizu
The concept of "watershed shift"(WS)has been proposed as a cause of the ischemic complications following a superficial temporal artery-middle cerebral artery(STA-MCA)bypass operation performed for the management of moyamoya disease. Previous reports have observed that only 1.2-5.7% of the patients who underwent a bypass operation for the management of moyamoya disease developed cerebral infarction secondary to the WS phenomenon. To date, the WS phenomenon has not been objectively proven on imaging studies...
February 2018: No Shinkei Geka. Neurological Surgery
https://www.readbyqxmd.com/read/29435280/analysis-of-the-clinical-characteristics-of-hemorrhagic-moyamoya-disease-in-the-jilin-province-of-northeastern-china-a-single-center-study-of-212-cases
#2
Qinglian Li, Lai Qu, Yongjie Yuan, Baofeng Xu, Yunbao Guo, Kan Xu, Jinlu Yu
The present study aimed to investigate the clinical characteristics of hemorrhagic moyamoya disease (MMD) in Jilin province in northeast China. A total of 212 cases of hemorrhagic MMD were consecutively enrolled from the First Hospital of Jilin University in Changchun, China between January 2011 and January 2015. The patients' general clinical data, including age and gender characteristics, history of previous illnesses, hemorrhage type and onset symptoms, Hunt-Hess classification at admission, imaging characteristics, association with aneurysms, treatments and prognosis, were recorded and analyzed using SPSS 19...
February 2018: Biomedical Reports
https://www.readbyqxmd.com/read/29432946/postoperative-cerebral-infarction-risk-factors-and-postoperative-management-of-pediatric-moyamoya-disease-patients
#3
Shinsuke Muraoka, Yoshio Araki, Goro Kondo, Michihiro Kurimoto, Yoshiki Shiba, Kenji Uda, Shinji Ota, Sho Okamoto, Toshihiko Wakabayashi
OBJECT: Though revascularization surgery for moyamoya disease patients can effectively prevent ischemic events and thus improve the long-term clinical outcome, the incidence of postoperative ischemic complications affects patients' quality of life. This study aimed to clarify the risk factors associated with postoperative ischemic complications and to discuss the appropriate perioperative management. METHODS: Fifty-eight revascularization operations were performed in 37 children with moyamoya disease...
February 9, 2018: World Neurosurgery
https://www.readbyqxmd.com/read/29421412/right-subclavian-artery-aneurysms-with-fibromuscular-dysplasia
#4
Daisuke Kaneyuki, Hideki Ueda, Goro Matsumiya
Subclavian artery aneurysms are rare and even more uncommon in patients with fibromuscular dysplasia. A 20-year-old man with a past medical history of moyamoya disease, presented with an abnormal mass shadow in the apex of the right lung on chest x-ray. Based on computed tomography imaging, a diagnosis of right subclavian artery aneurysm was established and an excision of the aneurysm was performed. Since the left vertebral artery is dominant, the proximal and distal right subclavian artery and right vertebral artery were clamped...
February 5, 2018: Annals of Vascular Surgery
https://www.readbyqxmd.com/read/29395647/expression-of-connexin43-in-cerebral-arteries-of-patients-with-moyamoya-disease
#5
Jiaqi Liao, Tao Hong, Jinxian Xu, Erming Zeng, Bin Tang, Wentao Lai
BACKGROUND AND PURPOSE: Moyamoya disease has a high incidence of cerebral vascular accident in children and adolescents, which can endanger the physical and mental health of children and adults seriously. However, the etiology and the pathogenesis of moyamoya disease remain unclear. Connexin43 (Cx43) is a predominant intercellular gap junction protein that plays an important role in the normal function of arteries and the development of several cardiovascular diseases. We aimed to preliminarily investigate pathological changes and the expression of Cx43 in cerebral arteries of patients with moyamoya disease...
January 25, 2018: Journal of Stroke and Cerebrovascular Diseases: the Official Journal of National Stroke Association
https://www.readbyqxmd.com/read/29390537/anca-positive-relapsing-polychondritis-graves-disease-and-suspected-moyamoya-disease-a-case-report
#6
Yi-Yi Xuan, Tian-Fang Li, Lei Zhang, Sheng-Yun Liu
RATIOINALE: Relapsing polychondritis (RP) is a rare and heterogeneous disease complex of unknown origin which basically affects cartilaginous structures, 40% of which accompanied by rheumatic, hematologic, and endocrine disease. Among them, vasculitis is the most common accompanying type and usually presented with positive antineutrophilic cytoplasmic antibody (ANCA). The presence of ANCA could be primary or drug-induced like propylthiouracil (PTU). Central involvement of RP is very rare, and there is almost no report of cerebral vasculopathy manifested as moyamoya...
December 2017: Medicine (Baltimore)
https://www.readbyqxmd.com/read/29387438/novel-and-recurrent-rnf213-variants-in-japanese-pediatric-patients-with-moyamoya-disease
#7
Hiroyuki Akagawa, Maki Mukawa, Tadashi Nariai, Shunsuke Nomura, Yasuo Aihara, Hideaki Onda, Taku Yoneyama, Takumi Kudo, Kazutaka Sumita, Taketoshi Maehara, Takakazu Kawamata, Hidetoshi Kasuya
Moyamoya disease is a progressive steno-occlusive condition of the main intracranial arteries that results in the compensatory formation of fragile moyamoya vessels at the base of the brain. RNF213 is the most significant susceptibility gene and is often found with the p.Arg4810Lys founder variant in East Asian patients. We identified three putatively deleterious variants of this gene from three pediatric patients: two were novel, and one was a recurrent missense variant previously reported in other pediatric patients...
2018: Human Genome Variation
https://www.readbyqxmd.com/read/29383984/preoperatively-reduced-cerebrovascular-contractile-reactivity-to-hypocapnia-by-hyperventilation-is-associated-with-cerebral-hyperperfusion-syndrome-after-arterial-bypass-surgery-for-adult-patients-with-cerebral-misery-perfusion-due-to-ischemic-moyamoya-disease
#8
Shinpei Sato, Daigo Kojima, Yasuyoshi Shimada, Jun Yoshida, Kentaro Fujimato, Shunrou Fujiwara, Masakazu Kobayashi, Yoshitaka Kubo, Kenji Yoshida, Kazunori Terasaki, Shouta Tsutsui, Kenya Miyoshi, Kuniaki Ogasawara
The present study examined whether preoperatively reduced cerebrovascular contractile reactivity to hypocapnia by hyperventilation is associated with development of cerebral hyperperfusion syndrome after arterial bypass surgery for adult patients with cerebral misery perfusion due to ischemic moyamoya disease. Among 65 adult patients with ischemic moyamoya disease, 19 had misery perfusion in the precentral region on preoperative 15O positron emission tomography and underwent arterial bypass surgery for that region...
January 1, 2018: Journal of Cerebral Blood Flow and Metabolism
https://www.readbyqxmd.com/read/29379567/rare-presentation-of-moyamoya-disease-with-sub-acute-presentation-in-iran
#9
Payam Sasannejad, Fateme Rezaei, Reza Bidaki, Ehsan Zarepur
Moyamoya disease is a chronic progressive vascular disease of brain characterized by bilateral stenosis or occlusion of the arteries around the circle of Willis with prominent arterial collateral circulation. We introduce here a patient with Moyamoya who was misdiagnosed. She was a 16-yr-old female from north east of Iran who complained left hemiparesis and was diagnosed Moyamoya disease by brain and cervical CT-Angiography. There was still great difficulty in the diagnosis of diffuse white matter lesions. The CT-Angiography showed bilateral internal carotid stenosis with "puff of smoke" collateralization arising from the circle of Willis, therefore Moyamoya disease was raised...
2018: Iranian Journal of Child Neurology
https://www.readbyqxmd.com/read/29374799/application-of-ct-perfusion-to-assess-hemodynamics-in-symptomatic-moyamoya-syndrome-focus-on-affected-side-and-parameter-characteristic
#10
Shuran Huang, Lingyun Gao, Yueqin Chen, Xiang Guo, Deguo Liu, Jiehuan Wang, Zhitao Shi, Zhanguo Sun, Feng Jin, Weijian Chen, Yunjun Yang
OBJECTIVE: Vascular and hemodynamic changes were not consistent in symptomatic and non-symptomatic cerebral hemisphere in patients with symptomatic moyamoya syndrome (MMS). Thus, the purpose of this study is to evaluate the hemodynamic difference between symptomatic and non-symptomatic cerebral hemisphere in patients with symptomatic MMS. METHODS: Patients who were diagnosed with symptomatic MMS were retrospectively collected. All cases underwent CTP examination...
January 27, 2018: Child's Nervous System: ChNS: Official Journal of the International Society for Pediatric Neurosurgery
https://www.readbyqxmd.com/read/29374613/default-mode-network-changes-in-moyamoya-disease-before-and-after-bypass-surgery%C3%A2-preliminary-report%C3%A2
#11
Yusuke Sakamoto, Sho Okamoto, Satoshi Maesawa, Epifanio Bagarinao, Yoshio Araki, Takashi Izumi, Hirohisa Watanabe, Gen Sobue, Toshihiko Wakabayashi
OBJECTIVE: Neurocognitive impairment is often reported in moyamoya disease. We aimed to detect default mode network (DMN) alterations using resting-state functional MRI (rsfMRI) and their association with neurocognitive impairments. Additionally, the influence of surgical treatment was individually evaluated. METHODS: Seven patients with moyamoya disease underwent preoperative rsfMRI and neuropsychological tests. We compared the resting-state networks (RSNs) of our patients with those obtained from relatively large cohort datasets (127 healthy controls) using group independent component analysis (ICA) with dual regression analysis...
January 25, 2018: World Neurosurgery
https://www.readbyqxmd.com/read/29371256/comparison-of-blood-oxygenation-level-dependent-fmri-and-provocative-dsc-perfusion-mr-imaging-for-monitoring-cerebrovascular-reserve-in-intracranial-chronic-cerebrovascular-disease
#12
K R Thulborn, I C Atkinson, A Alexander, M Singal, S Amin-Hanjani, X Du, A Alaraj, F T Charbel
BACKGROUND AND PURPOSE: Loss of hemodynamic reserve in intracranial cerebrovascular disease reduces blood oxygenation level-dependent activation by fMRI and increases asymmetry in MTT measured by provocative DSC perfusion MR imaging before and after vasodilation with intravenous acetazolamide. The concordance for detecting hemodynamic reserve integrity has been compared. MATERIALS AND METHODS: Patients (n = 40) with intracranial cerebrovascular disease and technically adequate DSA, fMRI and provocative DSC perfusion studies were retrospectively grouped into single vessels proximal to and distal from the circle of Willis, multiple vessels, and Moyamoya disease...
January 25, 2018: AJNR. American Journal of Neuroradiology
https://www.readbyqxmd.com/read/29371165/occipital-artery-to-middle-cerebral-artery-bypass-in-cases-of-unavailable-superficial-temporal-artery
#13
Tsukasa Hirano, Takeshi Mikami, Hime Suzuki, Toru Hirano, Yusuke Kimura, Katusya Komatsu, Yukinori Akiyama, Masahiko Wanibuchi, Nobuhiro Mikuni
In neurosurgery, extracranial-to-intracranial (EC-IC) bypass surgery is necessary for patients who have undergone surgery in which the superficial temporal artery (STA) was already used for a different bypass procedure or was damaged. Here, we report our experience with EC-IC bypass using the occipital artery (OA) in cases in which the STA is unavailable, and discuss the technical considerations and pitfalls. Five patients with ischemic-onset moyamoya disease and atherosclerotic disease were included. Two patterns of skin incisions were planned according to the OA pathway and recipient artery location...
January 22, 2018: World Neurosurgery
https://www.readbyqxmd.com/read/29369424/non-contrast-enhanced-4d-intracranial-mr-angiography-based-on-pseudo-continuous-arterial-spin-labeling-with-the-keyhole-and-view-sharing-technique
#14
Makoto Obara, Osamu Togao, Gabriele M Beck, Shuhei Shibukawa, Tomoyuki Okuaki, Masami Yoneyama, Masanobu Nakamura, Hiroshi Honda, Marc Van Cauteren
PURPOSE: 4D dynamic MR angiography (4D-MRA) using pseudo-continuous arterial spin labeling (pCASL), combined with Keyhole and View-sharing (4D-PACK) for scan acceleration, is introduced. Its validity for arterial inflow dynamics visualization was investigated through comparison with 4D-pCASL and contrast inherent inflow enhanced multiphase angiography (CINEMA). METHODS: Six healthy volunteers were included in the study. The arterial transit time (ATT) in 4D-PACK was measured at multiple regions in middle cerebral artery (MCA), and Pearson's correlation coefficient with ATT in 4D-pCASL was calculated...
January 25, 2018: Magnetic Resonance in Medicine: Official Journal of the Society of Magnetic Resonance in Medicine
https://www.readbyqxmd.com/read/29366619/encephaloduroateriosynangiosis-versus-conservative-treatment-for-patients-with-moyamoya-disease-at-late-suzuki-stage
#15
Peicong Ge, Xun Ye, Qian Zhang, Dong Zhang, Shuo Wang, Jizong Zhao
The purpose of this study is to investigate the long-term outcomes after conservative and encephaloduroateriosynangiosis procedures for patients with moyamoya disease at late Suzuki stage. We retrospectively reviewed 64 patients (128 hemispheres) with moyamoya disease at late Suzuki Stage at Beijing Tiantan Hospital. Clinical features, radiologic findings, and outcomes were analyzed. The mean age at diagnosis was 29.0 ± 14.9 years. The distribution of the initial Suzuki stage of MMD was as follows: stage 4, n = 75; stage 5, n = 46; stage 6, n = 7, PCA involvement was observed in 4 (37...
January 20, 2018: Journal of Clinical Neuroscience: Official Journal of the Neurosurgical Society of Australasia
https://www.readbyqxmd.com/read/29364453/moyamoya-syndrome-associated-with-neurofibromatosis-type-1-in-a-pediatric-patient
#16
Natália Battisti Serafini, Cássio Battisti Serafini, Alanna Santoro Vinhas, Marcio Barbosa Godinho
Neurofibromatosis type 1 is a multisystem genetic disease of autosomal dominant transmission that reveals important cutaneous manifestations such as café-au-lait spots, multiple neurofibromas, and ephelides in skin fold areas, as well as hamartomatous lesions in the eyes, bones, glands, and central nervous system. Moyamoya disease is a rare progressive vaso-occlusive disorder that occurs with important ischemic cerebrovascular events. Despite the rarity of this association in childhood, children diagnosed with neurofibromatosis type 1 and focal neurologic symptoms should be investigated for moyamoya syndrome...
November 2017: Anais Brasileiros de Dermatologia
https://www.readbyqxmd.com/read/29362841/spectrum-of-cerebral-arterial-and-venous-abnormalities-in-alagille-syndrome
#17
Candice D Carpenter, Luke L Linscott, James L Leach, Sudhakar Vadivelu, Todd Abruzzo
BACKGROUND: Alagille syndrome is a pediatric multisystem disease with increased prevalence of cerebrovascular disease. The spectrum of cerebrovascular disease in Alagille syndrome includes cerebral aneurysms, moyamoya arteriopathy and dolichoectasia. The prevalence of cerebrovascular disease in Alagille syndrome varies widely in the literature. OBJECTIVE: To determine the prevalence of cerebrovascular disease in our institution's Alagille patient population by employing a full primary review of all available neuroimaging...
January 23, 2018: Pediatric Radiology
https://www.readbyqxmd.com/read/29353860/association-of-hyperthyroidism-and-thyroid-autoantibodies-with-moyamoya-disease-and-its-stroke-event-a-population-based-case-control-study-and-meta-analysis
#18
Jun Hyong Ahn, Jin Pyeong Jeon, Jeong Eun Kim, Eun Jin Ha, Won-Sang Cho, Young Joo Park, Nam Han Cho, Hoon Sung Choi, Hyun-Seung Kang, Young-Je Son, Jae Seung Bang, Chang Wan Oh
The aim of this study was to investigate the specific thyroid condition and thyroid autoantibodies in adult moyamoya disease (MMD) according to clinical presentation (ischemia vs. hemorrhage stroke). In addition, a meta-analysis was performed to reveal the association between adult MMD and elevated thyroid function, or autoantibodies. Prospectively collected data on 169 consecutive patients with MMD at a single institution were analyzed. Community-based controls matched for age and sex were selected for comparison...
January 19, 2018: Neurologia Medico-chirurgica
https://www.readbyqxmd.com/read/29351682/radial-artery-fascial-flow-through-free-flap-for-combined-revascularization-in-moyamoya-disease
#19
Jonathan Russin, Joseph Carey
BACKGROUND: Free flaps are commonly used by other surgical subspecialties for soft tissue reconstruction and revascularization. Cranial applications of these flaps have been limited to only a single case report. OBJECTIVE: To present a new technique for combined revascularization in moyamoya disease using a flow-through free flap. METHODS: Data were obtained from an Institutional Review Board-approved, prospectively maintained database with informed consent from the patient...
February 1, 2018: Operative Neurosurgery (Hagerstown, Md.)
https://www.readbyqxmd.com/read/29351284/magnetic-resonance-angiography-with-compressed-sensing-an-evaluation-of-moyamoya-disease
#20
Takayuki Yamamoto, Tomohisa Okada, Yasutaka Fushimi, Akira Yamamoto, Koji Fujimoto, Sachi Okuchi, Hikaru Fukutomi, Jun C Takahashi, Takeshi Funaki, Susumu Miyamoto, Aurélien F Stalder, Yutaka Natsuaki, Peter Speier, Kaori Togashi
Compressed sensing (CS) reconstructions of under-sampled measurements generate missing data based on assumptions of image sparsity. Non-contrast time-of-flight MR angiography (TOF-MRA) is a good candidate for CS based acceleration, as MRA images feature bright trees of sparse vessels over a well-suppressed anatomical background signal. A short scan time derived from CS is beneficial for patients of moyamoya disease (MMD) because of the frequency of MR scans. The purpose of this study was to investigate the reliability of TOF-MRA with CS in the evaluation of MMD...
2018: PloS One
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