Gabrielle Norrish, Tao Ding, Ella Field, Lidia Ziólkowska, Iacopo Olivotto, Giuseppe Limongelli, Aristides Anastasakis, Robert Weintraub, Elena Biagini, Luca Ragni, Terence Prendiville, Sophie Duignan, Karen McLeod, Maria Ilina, Adrián Fernández, Regina Bökenkamp, Anwar Baban, Peter Kubuš, Piers E F Daubeney, Georgia Sarquella-Brugada, Sergi Cesar, Chiara Marrone, Vinay Bhole, Constancio Medrano, Orhan Uzun, Elspeth Brown, Ferran Gran, Francisco J Castro, Graham Stuart, Gabriele Vignati, Roberto Barriales-Villa, Luis G Guereta, Satish Adwani, Katie Linter, Tara Bharucha, Pablo Garcia-Pavia, Torsten B Rasmussen, Margherita M Calcagnino, Caroline B Jones, Hans De Wilde, J Toru-Kubo, Tiziana Felice, Jens Mogensen, Sujeev Mathur, Zdenka Reinhardt, Constantinos O'Mahony, Perry M Elliott, Rumana Z Omar, Juan P Kaski
Importance: Sudden cardiac death (SCD) is the most common mode of death in childhood hypertrophic cardiomyopathy (HCM), but there is no validated algorithm to identify those at highest risk. Objective: To develop and validate an SCD risk prediction model that provides individualized risk estimates. Design, Setting, and Participants: A prognostic model was developed from a retrospective, multicenter, longitudinal cohort study of 1024 consecutively evaluated patients aged 16 years or younger with HCM...
August 14, 2019: JAMA Cardiology