Zeinab Afify, Manuela Orjuela-Grimm, Christine Moore Smith, Mansi Dalal, James B Ford, Pallavi Pillai, Joanna M Robles, Sonika Reddy, Sarah McCormack, Matthew J Ehrhardt, Tonya Ureda, Warren Alperstein, Holly Edington, Tamara P Miller, Jeremy D Rubinstein, Madison Kavanaugh, Andrew J Bukowinski, Erika Friehling, Julie M Rivers, Karen M Chisholm, Lianna J Marks, Clinton C Mason
Burkitt lymphoma arising in paediatric post-solid-organ transplantation-Burkitt lymphoma (PSOT-BL) is a clinically aggressive malignancy and a rare form of post-transplant lymphoproliferative disorder (PTLD). We evaluated 35 patients diagnosed with PSOT-BL at 14 paediatric medical centres in the United States. Median age at organ transplantation was 2.0 years (range: 0.1-14) and age at PSOT-BL diagnosis was 8.0 years (range: 1-17). All but one patient had late onset of PSOT-BL (≥2 years post-transplant), with a median interval from transplant to PSOT-BL diagnosis of 4...
December 1, 2022: British Journal of Haematology