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Congenital pulmonary airway malformation

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https://www.readbyqxmd.com/read/28195247/type-ii-congenital-pulmonary-airway-malformation-associated-with-intralobar-pulmonary-sequestration-report-of-a-case-and-review-of-classification-criteria
#1
M G Mastrogiulio, A Barone, M G Disanto, A Ginori, M R Ambrosio, S F Carbone, D Spina
Pulmonary congenital abnormalities are rare disorders including congenital pulmonary airway malformations (CPAM) and pulmonary sequestration (PS). CPAM is a lesion characterized by the presence of anomalous bronchiolar or acinar structures, variable in size, either cystic or not cystic. PS is generally defined as nonfunctioning lung tissue that is not in normal continuity with the tracheobronchial tree and that derives its blood supply from systemic vessels. We describe a case of a baby girl with a very rare association between CPAM type 2 and intralobar pulmonary sequestration (IPS) focusing on the cystic lesions typical of CPAM and on the lymphatic and blood vessels...
March 2016: Pathologica
https://www.readbyqxmd.com/read/28061000/prediction-of-neonatal-respiratory-distress-in-pregnancies-complicated-by-fetal-lung-masses
#2
Anna I Girsen, Susan R Hintz, Rami Sammour, Aasim Naqvi, Yasser Y El-Sayed, Katie Sherwin, Alexis S Davis, Valerie Y Chock, Richard A Barth, Erika Rubesova, Karl G Sylvester, Ritu Chitkara, Yair J Blumenfeld
OBJECTIVE: To evaluate the utility of fetal lung mass imaging for predicting neonatal respiratory distress. METHOD: Pregnancies with fetal lung masses between 2009 and 2014 at a single center were analyzed. Neonatal respiratory distress was defined as: Intubation and mechanical ventilation at birth, surgery before discharge, or ECMO. The predictive utility of the initial as well as maximal lung mass volume and congenital pulmonary airway malformation (CPAM) volume ratio (CVR) by US and MRI was analyzed...
January 6, 2017: Prenatal Diagnosis
https://www.readbyqxmd.com/read/28045420/a-case-of-tracheal-bronchus-associated-with-right-aortic-arch-and-partial-anomalous-pulmonary-venous-connection
#3
Vehbi Doğan, İlker Ertuğrul, Yasemin Taşcı Yıldız, Utku Arman Örün, Selmin Karademir
Tracheal bronchus includes a variety of bronchial anomalies arising in the trachea or main bronchus and directed toward the upper-lobe territory. Reported incidence varies from 1-3% in the pediatric population. It is generally associated with other congenital malformations, including costovertebral anomalies, congenital airway and lung anomalies, vascular anomalies, and congenital heart defects. Presently described was the case of a 14-year-old female with tracheal right-upper-lobe bronchus, right aortic arch with mirror image, and abnormal left upper pulmonary venous return to innominate vein...
December 2016: Türk Kardiyoloji Derneği Arşivi: Türk Kardiyoloji Derneğinin Yayın Organıdır
https://www.readbyqxmd.com/read/28040831/pulmonary-lobectomy-techniques-in-infants-and-children
#4
Atsuyuki Yamataka, Hiroyuki Koga, Takanori Ochi, Kota Imashimizu, Kazuhiro Suzuki, Ryohei Kuwatsuru, Geoffrey Lane, Kinya Nishimura, Eiichi Inada, Kenji Suzuki
Thoracoscopic pulmonary lobectomy (TPL) techniques in infants and children are presented practically with concise descriptions and numerous illustrations. TPL is the treatment of choice for congenital pulmonary airway malformation and intralobar pulmonary sequestration, both now commonly diagnosed prenatally. Timing of surgery is somewhat controversial in asymptomatic cases with small isolated lesions. Incomplete fissures and history of chest infections are most problematic. Thorough understanding of anatomic relations preoperatively is vital for successful outcome and thin-slice computed tomography with 3D reconstruction of vessels is valuable...
December 31, 2016: Pediatric Surgery International
https://www.readbyqxmd.com/read/28029591/cardiorespiratory-interactions-in-paediatrics-it-s-almost-always-the-circulation-stupid
#5
REVIEW
M L Rigby, M Rosenthal
The interaction of the heart and lungs is probably the most important aspect of life and survival. Fortunately, it is not difficult to understand the fundamentals. The purpose of the lungs and their ventilation is to present oxygen to the circulation via the alveoli and to receive carbon dioxide from the circulation and then expel it. The relations of the heart and lungs and the matching of blood flow to the various organs with ventilation and lung perfusion may be disrupted by a variety of congenital or acquired heart malformations...
August 12, 2016: Paediatric Respiratory Reviews
https://www.readbyqxmd.com/read/27973931/anesthetic-management-of-a-patient-with-emanuel-syndrome
#6
Masanori Tsukamoto, Takashi Hitosugi, Kanako Esaki, Takeshi Yokoyama
Emanuel syndrome is associated with supernumerary chromosome, which consists of the extra genetic material from chromosome 11 and 22. The frequency of this syndrome has been reported as 1 in 110,000. It is a rare anomaly associated with multiple systemic malformations such as micrognathia and congenital heart disease. In addition, patients with Emanuel syndrome may have seizure disorders. We experienced anesthetic management of a patient with Emanuel syndrome who underwent palatoplasty. This patient had received tracheotomy due to micrognathia...
2016: Anesthesia Progress
https://www.readbyqxmd.com/read/27833903/virtual-3d-modeling-of-airways-in-congenital-heart-defects
#7
Simone Speggiorin, Saravanan Durairaj, Branko Mimic, Antonio F Corno
The involvement of the airway is not uncommon in the presence of complex cardiovascular malformations. In these cases, a careful inspection of the relationship between the airway and the vasculature is paramount to plan the surgical procedure. Three-dimensional printing enhanced the visualization of the cardiovascular structure. Unfortunately, IT does not allow to remove selected anatomy to improve the visualization of the surrounding ones. Computerized modeling has the potential to fill this gap by allowing a dynamic handling of different anatomies, increasing the exposure of vessels or bronchi to show their relationship...
2016: Frontiers in Pediatrics
https://www.readbyqxmd.com/read/27772928/congenital-pulmonary-airway-malformation-a-study-of-2-cases
#8
Priya J Padma, Manna Valiathan, Vijay Kumar
No abstract text is available yet for this article.
February 2016: Pathology
https://www.readbyqxmd.com/read/27770196/is-congenital-pulmonary-airway-malformation-really-a-rare-disease-result-of-a-prospective-registry-with-universal-antenatal-screening-program
#9
C T Lau, A Kan, N Shek, P Tam, K K Y Wong
BACKGROUND: Congenital pulmonary airway malformation (CPAM) is an increasingly recognized disease with potential mortality. Owing to limited published studies, the true incidence is yet to be determined. We carried out this prospective study with the aim to estimate its true incidence on a population basis. METHODS: An antenatal ultrasonography program was implemented since 2009. Fetuses with suspected intra-thoracic lesions were monitored by regular follow-ups...
October 21, 2016: Pediatric Surgery International
https://www.readbyqxmd.com/read/27723920/antenatally-detected-congenital-pulmonary-airway-malformations-the-oxford-experience
#10
Hemanshoo Sudhir Thakkar, Jonathan Durell, Subhasis Chakraborty, Bianca-Lea Tingle, Arnwald Choi, Darren J Fowler, Steve J Gould, Lawrence Impey, Kokila Lakhoo
Congenital airway pulmonary malformations are increasingly being diagnosed, but their management continues to remain controversial. Our approach has been to offer surgery to mitigate the risk of infection and possible malignancy. All patients routinely undergo a CT scan of the chest postnatally and once the diagnosis is confirmed, minimal access surgery is offered. Our anesthetists provide single-lung ventilation to enhance the operative view. We conducted a retrospective review over a 10-year period, during which 91 patients were prenatally suspected to have a cystic lung lesion...
October 10, 2016: European Journal of Pediatric Surgery
https://www.readbyqxmd.com/read/27671988/congenital-pulmonary-airway-malformation-cpam-with-initial-presentation-in-an-adult-a-rare-presentation-of-a-rare-disease
#11
Mohannad Abu Omar, Emily Tylski, Mouhanna Abu Ghanimeh, Ashraf Gohar
Congenital pulmonary airway malformation (CPAM) is a rare congenital abnormality with unknown exact aetiology or clear genetic association. It is characterised by a failure of bronchial development and localised glandular overgrowth. Typically, it is diagnosed on prenatal ultrasound, only infrequently in children, and even less commonly in adults. We present a case of a 25-year-old man, with no previous lung diseases who presented with right-sided chest pain, fever and cough suggestive of pulmonary infection...
September 26, 2016: BMJ Case Reports
https://www.readbyqxmd.com/read/27645976/pulmonary-kirsten-rat-sarcoma-virus-mutation-positive-mucinous-adenocarcinoma-arising-in-a%C3%A2-congenital-pulmonary-airway%C3%A2-malformation-mixed-type-1-and-2
#12
Gopal Singh, Amy Coffey, Robert Neely, Daniel Lambert, Joshua Sonett, Alain C Borczuk, Lyall Gorenstein
Congenital pulmonary airway malformation (CPAM) is a developmental abnormality of the lung, which results from an abnormality of branching during fetal development of the lung. We report the case of an 18 year-old woman who developed Kirsten rat sarcoma virus (KRAS) mutation positive mucinous adenocarcinoma of the lung (AC) in association with mixed CPAM type 1 and 2. This case is unique as KRAS mutation positive AC is present in a setting of both CPAM 1 and 2 in the same lesion.
October 2016: Annals of Thoracic Surgery
https://www.readbyqxmd.com/read/27577236/reply-to-the-letter-to-the-editor-type-i-pleuropulmonary-blastoma-versus-congenital-pulmonary-airway-malformation-type-iv
#13
Ruben Lamas-Pinheiro, Mafalda David, Tiago Henriques-Coelho
No abstract text is available yet for this article.
2017: Neonatology
https://www.readbyqxmd.com/read/27562209/type-i-pleuropulmonary-blastoma-versus-congenital-pulmonary-airway-malformation-type-iv
#14
Louis P Dehner, Yoav H Messinger, Gretchen M Williams, Douglas R Stewart, Laura A Harney, Kris Ann Schultz, D Ashley Hill
No abstract text is available yet for this article.
2017: Neonatology
https://www.readbyqxmd.com/read/27490105/congenital-cystic-lung-lesions-evolution-from-in-utero-to-pathology-diagnosis-a-multidisciplinary-approach
#15
Steven Hardee, Lea Tuzovic, Cicero T Silva, Robert A Cowles, Joshua Copel, Raffaella A Morotti
Congenital cystic lung lesions (CCLL) are a group of rare pathologies that are usually diagnosed in the pre-natal period. The majority of these lesions are diagnosed at pathology examination as congenital pulmonary airway malformations (CPAM) and bronchopulmonary sequestration (BPS). These lesions are typically managed by surgical intervention within the first year of life and have an excellent prognosis. We examined the evolution of imaging appearances from prenatal diagnosis to postnatal work-up of these lesions and correlate imaging and pathological findings...
August 4, 2016: Pediatric and Developmental Pathology
https://www.readbyqxmd.com/read/27469386/refractory-tension-pneumothorax-as-a-result-of-an-internally-displaced-thoracoamniotic-shunt-in-an-infant-with-a-congenital-pulmonary-airway-malformation
#16
Brenda Hiu Yan Law, Ioana Bratu, Venu Jain, Marc-Antoine Landry
Antenatally, congenital pulmonary airway malformation (CPAM) causing fetal hydrops can be palliated with thoracoamniotic shunts, which may become displaced in utero. We report a case of an infant born at 34 weeks gestational age with an antenatally diagnosed macrocystic lung lesion, fetal hydrops and an internally displaced thoracoamniotic shunt. The infant suffered refractory pneumothoraces despite multiple chest drains, and stabilised only after surgical resection of the lesion. Intraoperatively, the shunt was noted to form a connection between a type I CPAM and the pleural space...
July 28, 2016: BMJ Case Reports
https://www.readbyqxmd.com/read/27458568/pulmonary-malformations-predictors-of-neonatal-respiratory-distress-and-early-surgery
#17
Sara Costanzo, Claudia Filisetti, Claudio Vella, Mariangela Rustico, Paola Fontana, Gianluca Lista, Salvatore Zirpoli, Marcello Napolitano, Giovanna Riccipetitoni
OBJECTIVES: The objective of our study is to retrospectively analyze a single-centre series of antenatally detected pulmonary malformations (PM) and to evaluate their postnatal outcome. MATERIALS AND METHODS: We retrospectively reviewed all prenatally diagnosed PM patients referred to our Centre in the period between January 1999 and December 2014. All cases were diagnosed by one of our Maternal-Fetal Specialists by US examination. Congenital pulmonary airway malformation (CPAM) volume ratio (CVR), development of fetal complications, need for fetal therapy, need for neonatal resuscitation and timing of surgery were analyzed...
July 2016: Journal of Neonatal Surgery
https://www.readbyqxmd.com/read/27343517/direct-tracheobronchopexy-and-posterior-descending-aortopexy-for-severe-left-mainstem-bronchomalacia-associated-with-congenital-pulmonary-airway-malformation-and-left-circumflex-aortic-arch
#18
Christopher W Baird, Sanjay Prabhu, Terry L Buchmiller, Charles Smithers, Russell Jennings
Complex tracheobronchial obstruction and malacia can be associated with conotruncal and aortic arch anomalies. A circumflex aortic arch composed of a left aortic arch and right descending aorta is an extremely rare anomaly that can severely affect the distal trachea and mainstem bronchi, resulting in severe respiratory symptoms. We report the case of a patient with circumflex aortic arch and severe left mainstem bronchial obstruction and malacia in which the external aortic compression and residual bronchomalacia were addressed with direct bronchial and tracheal intervention...
July 2016: Annals of Thoracic Surgery
https://www.readbyqxmd.com/read/27292597/resection-of-pediatric-lung-malformations-national-trends-in-resource-utilization-outcomes
#19
Amy E Wagenaar, Jun Tashiro, Shevonne S Satahoo, Juan E Sola, Holly L Neville, Anthony R Hogan, Eduardo A Perez
PURPOSE: We sought to determine factors influencing survival and resource utilization in patients undergoing surgical resection of congenital lung malformations (CLM). Additionally, we used propensity score-matched analysis (PSMA) to compare these outcomes for thoracoscopic versus open surgical approaches. METHODS: Kids' Inpatient Database (1997-2009) was used to identify congenital pulmonary airway malformation (CPAM) and pulmonary sequestration (PS) patients undergoing resection...
September 2016: Journal of Pediatric Surgery
https://www.readbyqxmd.com/read/27141433/congenital-pulmonary-airway-malformation-in-a-36-year-old-female
#20
Timothy J Barreiro, Lucas Henn, Sisham Ingnam, Michael Sypert
Congenital pulmonary airway malformation (CPAM), previously known as congenital cystic adenomatoid malformation (CCAM), is an inborn abnormality of the lower respiratory system. Most often diagnosed in the perinatal period, these anomalies usually present with tachypnea, cyanosis, and respiratory distress. However, rare cases are asymptomatic and undiagnosed until adulthood.
2016: Respiratory Medicine Case Reports
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