Valérie Devauchelle-Pensec, Xavier Mariette, Anas-Alexis Benyoussef, Sylvie Boisrame, Béatrice Cochener, Divi Cornec, Gaëtane Nocturne, Jacques Eric Gottenberg, Eric Hachulla, Pierre Labalette, Véronique Le Guern, Ruth M'Bwang Seppoh, Jacques Morel, Marie Orliaguet, Alain Saraux, Raphaèle Seror, Nathalie Costedoat-Chalumeau
Sjögren's disease (SD), also known as Sjögren's syndrome (SS) or Gougerot-Sjögren's syndrome in France, is a rare systemic autoimmune disease in its primary form and is characterised by tropism for the exocrine glandular epithelia, particularly the salivary and lacrimal glands. The lymphocytic infiltration of these epithelia will clinically translate into a dry syndrome which, associated with fatigue and pain, constitutes the symptom triad of the disease. In about one third of patients, SD is associated with systemic complications that can affect the joints, skin, lungs, kidneys, central or peripheral nervous system, and lymphoid organs with an increased risk of B-cell lymphoma...
August 2023: La Revue de Médecine Interne