Wei-Chun Huang, Song-Chou Hsieh, Yen-Wen Wu, Tsu-Yi Hsieh, Yih-Jer Wu, Ko-Jen Li, Min-Ji Charng, Wei-Sheng Chen, Shih-Hsien Sung, Yen-Po Tsao, Wan-Jing Ho, Chien-Chih Lai, Chin-Chang Cheng, Hung-Cheng Tsai, Chih-Hsin Hsu, Cheng-Hsun Lu, Yu-Wei Chiu, Chieh-Yu Shen, Chun-Hsien Wu, Feng-Cheng Liu, Yen-Hung Lin, Fu-Chiang Yeh, Wei-Shin Liu, Hui-Ting Lee, Shu-Hao Wu, Chi-Ching Chang, Chun-Yuan Chu, Charles Jia-Yin Hou, Chang-Youh Tsai
BACKGROUND: Pulmonary arterial hypertension (PAH), defined as the presence of a mean pulmonary artery pressure > 20 mmHg, pulmonary artery wedge pressure ≤ 15 mmHg, and pulmonary vascular resistance (PVR) > 2 Wood units based on expert consensus, is characterized by a progressive and sustained increase in PVR, which may lead to right heart failure and death. PAH is a well-known complication of connective tissue diseases (CTDs), such as systemic sclerosis, systemic lupus erythematosus, Sjogren's syndrome, and other autoimmune conditions...
March 2023: Acta Cardiologica Sinica