keyword
MENU ▼
Read by QxMD icon Read
search

Polyserositis in children

keyword
https://www.readbyqxmd.com/read/26114369/systemic-juvenile-idiopathic-arthritis-complicated-by-macrophage-activation-syndrome
#1
REVIEW
Linda Wagner-Weiner
Systemic juvenile idiopathic arthritis (sJIA) is characterized by a large range of extra-articular manifestations in addition to joint inflammation. The child with sJIA usually presents with a spiking fever pattern, evanescent rash, and arthralgias/arthritis. Other features often present are lymphadenopathy, hepatosplenomegaly, and polyserositis. The systemic manifestations are frequently more prominent and severe than the arthritis. Laboratory studies reflect systemic inflammation with significant anemia, and elevation of acute phase reactants, platelets, and white blood cell count...
June 2015: Pediatric Annals
https://www.readbyqxmd.com/read/26028444/febrile-seizures-in-children-with-familial-mediterranean-fever-coincidence-or-association
#2
Elif Çomak, Özlem Tüfekçi, Fatih Kılıçbay, Emel Isıyel, Ali Haydar Sever, Ayça Aslanger, Barış Ekici
BACKGROUND: Familial Mediterranean fever (FMF) is an inherited disease characterized by recurrent bouts of fever and polyserositis and caused by MEditerranean FeVer gene (MEFV) mutations. Given the febrile characteristics of the disease one would expect higher frequency of febrile seizure in this group of pediatric patients. OBJECTIVES: To evaluate the frequency of febrile seizure and related factors in patients with FMF. METHODS: The children with the diagnosis of FMF were enrolled in the study...
September 2015: European Journal of Paediatric Neurology: EJPN
https://www.readbyqxmd.com/read/23907647/patient-management-and-the-association-of-less-common-familial-mediterranean-fever-symptoms-with-other-disorders
#3
Mike M Moradian, Tamara Sarkisian, Gayane Amaryan, Hasmik Hayrapetyan, Anna Yeghiazaryan, Nairi Davidian, Nare Avanesian
PURPOSE: In this study, we present clinical data from 16,000 familial Mediterranean fever patients. We also discuss the clinical manifestation of a subset of these patients and their potential symptom associations with other disorders. METHODS: Familial Mediterranean fever patients were confirmed using Tel-Hashomer criteria and were tested for the 12 most common mutations using the familial Mediterranean fever StripAssay. A total of 100 samples were selected, and their MEFV gene exons and intron junctions were completely sequenced...
March 2014: Genetics in Medicine: Official Journal of the American College of Medical Genetics
https://www.readbyqxmd.com/read/23132478/clinical-and-laboratory-profile-of-children-with-eosinophilia-at-dhulikhel-hospital
#4
S Shrestha, Singh S Dongol, N C Shrestha, R P B Shrestha
BACKGROUND: Eosinophilia in children is commonly caused by or parasitic, allergic and immunologic problems. OBJECTIVES: To study clinical and laboratory profile of patients with eosinophilia and to identify possible causes. METHOD: A prospective and descriptive study was conducted from January 2009- December 2011. All the cases of eosinophilia with symptoms and signs of single or multiple organ were included. The known cause of eosinophilia like allergy, asthma and drugs were excluded...
April 2012: Kathmandu University Medical Journal (KUMJ)
https://www.readbyqxmd.com/read/22067271/qt-dispersion-and-cardiac-involvement-in-children-with-familial-mediterranean-fever
#5
Bülent Koca, Ozgür Kasapçopur, Süleyman Bakari, Emine Sönmez, Funda Oztunç, Ayşe Güler Eroğlu, Levent Saltik, Ozden Calay
Familial Mediterranean fever is a hereditary disease characterised by recurrent and self-terminated attacks of fever and polyserositis. An earlier study found that adult patients of Familial Mediterranean fever had an abnormally longer QT dispersion and corrected QT dispersion, markers for ventricular arrhythmogenicity. QT dispersion is a simple non-invasive arrhythmogenic marker that can be used to assess homogeneity of cardiac repolarisation; however, it has not been studied in children with Familial Mediterranean fever before...
August 2012: Cardiology in the Young
https://www.readbyqxmd.com/read/21972596/-retrospective-analysis-of-39-child-cases-of-paragonimiasis
#6
Mei Guo, Wei Wang, Jian-yu Jiang
Clinical data of 39 children with paragonimiasis treated in Chongqing Three Gorges Central Hospital during 2008-2010 were retrospectively analyzed. The cases aged from 3 to 10 years old, with 25 cases of polyserositis (64.1%), 14 cases of cerebral paragonimiasis (35.9%). Among the cases of polyserositis, all showed dyspnea,tachypnea and diminished respiration (100%). Other symptoms or signs included purulent pleurisy, orthopnea, restricted activity, distant heart sounds, purulent pericarditis, abdominal distension, and hepatomegaly...
August 2011: chinese Journal of Parasitology & Parasitic Diseases
https://www.readbyqxmd.com/read/21317656/diagnosis-and-management-of-familial-mediterranean-fever-integrating-medical-genetics-in-a-dedicated-interdisciplinary-clinic
#7
REVIEW
Neda Zadeh, Terri Getzug, Wayne W Grody
Familial Mediterranean fever is an autosomal recessive genetic disorder characterized by recurrent febrile polyserositis, especially prevalent in individuals of Mediterranean descent. Familial Mediterranean fever can have nonspecific manifestations that mimic many common acquired disorders such as infections, acute appendicitis, cholecystitis, and arthritis, which can delay diagnosis for many years and subject patients to extensive evaluations and even unnecessary surgery. Untreated familial Mediterranean fever can result in serious complications such as end-stage renal disease and malabsorption secondary to amyloid deposition in the kidneys and digestive tract, male and female infertility, and growth retardation in children...
March 2011: Genetics in Medicine: Official Journal of the American College of Medical Genetics
https://www.readbyqxmd.com/read/20194447/familial-mediterranean-fever-in-children-presenting-with-attacks-of-fever-alone
#8
Shai Padeh, Avi Livneh, Elon Pras, Yael Shinar, Merav Lidar, Olga Feld, Yackov Berkun
OBJECTIVE: Familial Mediterranean fever (FMF) is an inherited disease characterized by attacks of febrile polyserositis. In children, attacks of fever alone, or with headache and malaise, may precede other forms of attacks. Our objective was clinical and genetic characterization of FMF and its development in pediatric patients who first presented with attacks of fever alone. METHODS: Clinical characterization and MEFV genotype of all FMF patients < 16 years of age at disease onset and first presenting with attacks of fever alone were analyzed and compared for age, sex, and disease duration with matched FMF patients presenting with serositis at the onset of the disease...
April 2010: Journal of Rheumatology
https://www.readbyqxmd.com/read/19845843/familial-mediterranean-fever-gene-mutations-in-the-inner-northern-region-of-turkey-and-genotype-phenotype-correlation-in-children
#9
Resul Yilmaz, Samet Ozer, Huseyin Ozyurt, Unal Erkorkmaz, Semsettin Sahin
AIM: Familial Mediterranean fever (FMF) is an autosomal recessive disorder characterised by recurrent episodes of fever, polyserositis and rash. The aim of this study was to determine the most common mutations and clinical features, and their relationships. METHODS: The medical records of 78 patients were evaluated retrospectively. All of the patients had been diagnosed with FMF according to Tel Hashomer criteria between January 2005 and May 2008 in general paediatric clinics of the School of Medicine at Gaziosmanpasa University...
November 2009: Journal of Paediatrics and Child Health
https://www.readbyqxmd.com/read/19240979/skin-and-muscle-involvement-as-presenting-symptoms-in-four-children-with-familial-mediterranean-fever
#10
Salih Kavukcu, Mehmet Türkmen, Alper Soylu, Belde Kasap, Burçak Tatli Güneş
Familial Mediterranean fever (FMF) is an autosomal recessive disorder characterized by recurrent attacks of fever and polyserositis. It is the most frequent periodic fever syndrome. In FMF, sterile peritonitis, pleuritis and arthritis are frequently seen in addition to recurrent febrile attacks. Skin and muscle involvement is less common. Here, we report four patients presented with skin lesions or myalgia. Most striking findings in those patients are the absence of other major criteria for FMF and dominancy of skin lesions or myalgia...
July 2009: Clinical Rheumatology
https://www.readbyqxmd.com/read/16712551/adrenomedullin-and-total-nitrite-levels-in-children-with-familial-mediterranean-fever
#11
Ayşe Balat, Ismail Işlek, Mustafa Cekmen, Muhittin Yürekli, Deniz Tekin, Ali Muslu, Saime Sahinöz
AIM: Familial Mediterranean fever (FMF) is the most frequent periodic syndrome characterised by recurrent attacks of polyserositis. However, recent studies revealed that there might be an ongoing subclinical inflammation between the attacks. As nitric oxide (NO) and adrenomedullin (AM) are both synthesised in the endothelium, and mediates many functions within immune system, we considered them to be an interesting target of investigation in FMF. METHODS: Fifteen children with FMF receiving regular colchicine, ranging in age from 3 to 16 years, were investigated in comparison with 15 healthy age- and sex-matched controls...
May 2006: Journal of Paediatrics and Child Health
https://www.readbyqxmd.com/read/13911319/recurrent-polyserositis-periodic-disease-familial-mediterranean-fever-in-children
#12
T R SHAPIRO, E N EHRENFELD
No abstract text is available yet for this article.
September 1962: Pediatrics
https://www.readbyqxmd.com/read/7932940/acute-hepatitis-in-recurrent-hereditary-polyserositis-familial-mediterranean-fever
#13
J Neequaye, A E Jelly
The clinical features of two cases of Hereditary Recurrent Polyserositis HRP (Familial Mediterranean Fever) in related Yemeni children resident in Saudi Arabia are described. One presented with recurrent acute hepatitis, which has not been previously documented. These are the first cases of HRP reported in Arabs originating from the Arabian Peninsula.
August 1994: Journal of Tropical Pediatrics
https://www.readbyqxmd.com/read/7424194/-clinical-effects-of-anti-human-lymphocyte-globulin-in-the-treatment-of-collagenoses-in-childhood
#14
J Oppermann, P Exadaktylos, M John, W Rumler
9 children with collagenoses were first treated with AHLG "Dessau" in combination with corticosteroids and then with Imurek (azathioprine). The children seemed to be vitally endangered and suffered from panarteritis, dermatomyositis, polyserositis or corticosteroid-resistent systemic juvenile rheumatoid arthritis. As assessed by decrease of inflammation and clinical symptoms the treatment appeared in one case to be very good and in another good; in four other children it was good for a short period; in three children there was no effect at all...
January 1980: Zeitschrift Für Rheumatologie
https://www.readbyqxmd.com/read/7337326/-muscular-manifestations-of-familial-paroxysmal-polyserositis-two-cases-in-children-author-s-transl
#15
M Nathanson, G Scart, R Perelman
No abstract text is available yet for this article.
1981: Annales de Médecine Interne
https://www.readbyqxmd.com/read/5565196/-evaluation-of-several-blood-coagulation-indices-in-children-with-rheumatic-polyserositis
#16
L S Novikova, E A Kovaleva
No abstract text is available yet for this article.
February 1971: Pediatriia
https://www.readbyqxmd.com/read/2663516/familial-mediterranean-fever-recurrent-hereditary-polyserositis-in-children-analysis-of-88-cases
#17
REVIEW
H A Majeed, M Barakat
The clinical profile, course and complications of familial Mediterranean fever (recurrent hereditary polyserositis) seen in 88 children over a period of 11 years are presented. Forty eight children (55%) started their illness below the age of 5 years, and the mean age of onset was 4.9 years. Peritonitis occurred in 85% of children, arthritis in 50%, pleuritis in 33% and erysipelas-like lesions in 16%. Two children developed renal amyloidosis, and one third of the children were subjected to unnecessary operative surgery, reflecting the diagnostic difficulties...
June 1989: European Journal of Pediatrics
https://www.readbyqxmd.com/read/2263427/short-course-chemotherapy-for-childhood-tuberculosis
#18
J Biddulph
A prospective study, with an attempted 24-month-post-treatment follow-up, of children with tuberculosis (TB) treated with short course chemotherapy (SCC) for 6 months was carried out because published experience of SCC in childhood TB was limited. All children in Port Moresby diagnosed as having TB between November, 1984, and November, 1986, entered the trial. Of the 639 children 165 (26%) were younger than 2 years old. Of these, 227 (35%) had extrapulmonary TB (peripheral lymph node, 110; central nervous system, 43; abdominal, 27; miliary, 16; bone and joint, 11; pleural, 11; polyserositis, 9)...
November 1990: Pediatric Infectious Disease Journal
https://www.readbyqxmd.com/read/2217666/the-cutaneous-manifestations-in-children-with-familial-mediterranean-fever-recurrent-hereditary-polyserositis-a-six-year-study
#19
H A Majeed, Z Quabazard, Z Hijazi, S Farwana, F Harshani
In a six-year study of 46 children with familial Mediterranean fever (recurrent hereditary polyserositis), 20 children (43 per cent) developed cutaneous manifestations. Ten children had 18 episodes of erysipelas-like erythema which proved to be specific for the disease. Twelve children (26 per cent) had 31 episodes of non-specific purpuric rash and six children (13 per cent) had nine episodes of Henoch-Schönlein purpura. Other manifestations included diffuse erythema of the face, and/or trunk, angioneurotic oedema, diffuse erythema of the palms and soles followed by mild desquamation of the skin, Raynaud's phenomenon and a subcutaneous nodule...
June 1990: Quarterly Journal of Medicine
https://www.readbyqxmd.com/read/2112191/long-term-colchicine-prophylaxis-in-children-with-familial-mediterranean-fever-recurrent-hereditary-polyserositis
#20
H A Majeed, J E Carroll, F A Khuffash, Z Hijazi
No abstract text is available yet for this article.
June 1990: Journal of Pediatrics
keyword
keyword
11285
1
2
Fetch more papers »
Fetching more papers... Fetching...
Read by QxMD. Sign in or create an account to discover new knowledge that matter to you.
Remove bar
Read by QxMD icon Read
×

Search Tips

Use Boolean operators: AND/OR

diabetic AND foot
diabetes OR diabetic

Exclude a word using the 'minus' sign

Virchow -triad

Use Parentheses

water AND (cup OR glass)

Add an asterisk (*) at end of a word to include word stems

Neuro* will search for Neurology, Neuroscientist, Neurological, and so on

Use quotes to search for an exact phrase

"primary prevention of cancer"
(heart or cardiac or cardio*) AND arrest -"American Heart Association"