Mary C Theroux, Sabina DiCindio, Lauren W Averill, Christian Pizarro, Abraham Oommen, Michael B Bober, Colleen Ditro, Jeffrey Campbell, Angela L Duker, Taylor Jones, Vandna Passi, Patrick Barth, Richard J Schmidt, Mary Little, Stuart Mackenzie, Shunji Tomatsu, William G Mackenzie
BACKGROUND: Recently, tracheal narrowing has been recognized as a significant comorbid condition in patients with Morquio A, also known as mucopolysaccharidosis IVA. We studied a large cohort of patients with Morquio A to describe the extent of their tracheal narrowing and its relationship to airway management during anesthesia care. METHODS: This is an observational study, collecting data retrospectively, of a cohort of patients with Morquio A. Ninety-two patients with Morquio A syndrome were enrolled, among whom 44 patients had their airway evaluated by computed tomography angiography and had undergone an anesthetic within a year of the evaluation...
November 1, 2023: Anesthesia and Analgesia