keyword
https://read.qxmd.com/read/35936618/chronic-t-cell-encephalitis-responsive-to-immunotherapy
#21
Arunmozhimaran Elavarasi, Garima Shukla, Deepti Vibha, Vaishali Suri, Chandra Sekhar Bal
Chronic encephalitis manifesting as an epilepsy syndrome most commonly presents as Rasmussen's syndrome, usually characterized by epilepsia partialis continua, hemiparesis, and progressive cortical deficits such as aphasia, hemianopia, and cognitive decline. It is characterized by progressive hemispheric cortical atrophy on imaging and is usually seen in childhood. Adult-onset of the syndrome is rare, and only a few cases have been reported with bilateral symptoms. We present a patient with pseudobulbar affect and frontal lobe dysfunction who developed multifocal myoclonic jerks, right hemibody focal motor seizures, and right hemiparesis with bilateral cerebellar signs...
May 2022: Annals of Indian Academy of Neurology
https://read.qxmd.com/read/35923344/role-of-diagnostic-imaging-in-rasmussen-s-encephalitis-a-case-report-from-nepal
#22
Suraj Sharma, Prakash Dhakal, Sajiva Aryal, Seema Bhandari, Abhishek Sharma
Rasmussen's encephalitis (RE) is a relatively rare chronic inflammatory neurological disease that usually only affects one hemisphere of the brain. It primarily affects children under the age of 10, although it can also affect teens and adults, causing drug-resistant seizures, progressive hemiparesis, and dementia. RE presents as a challenging diagnosis with MRI as the cornerstone of the evaluation and nuclear imaging as a complementary tool. We'd like to present a case of a 12-year-old girl who was diagnosed with RE after an MRI...
October 2022: Radiology Case Reports
https://read.qxmd.com/read/35918155/child-neurology-presurgical-evaluation-of-dominant-hemisphere-function-in-a-child-with-rasmussen-encephalitis-using-magnetoencephalography
#23
JOURNAL ARTICLE
Spriha Pavuluri, Valentina Gumenyuk, Sookyong Koh, Afshin Salehi, Sahara Cathcart, Olga Taraschenko
Rasmussen's encephalitis (RE) is a devastating progressive inflammatory disorder that leads to debilitating neurological deficits and intractable epilepsy. Surgical treatment of the dominant hemisphere has been attempted with hesitation given the lack of effective diagnostic tools to determine the potential functional deficits from disconnection procedures.We present the case of a 15-year-old male with RE, right hemiparesis, profound aphasia, and recurrent status epilepticus, who underwent language assessment using magnetoencephalography (MEG) prior to urgent hemispherectomy for epilepsia partialis continua...
August 2, 2022: Neurology
https://read.qxmd.com/read/35690982/cerebral-hemangiopericytoma-manifesting-as-epilepsia-partialis-continua-a-case-report
#24
JOURNAL ARTICLE
Prabhat Poudel, Sushan Shrestha, Maya Bhattachan
Cerebral hemangiopericytomas are very rare mesenchymal tumours arising from pericytes surrounding the blood vessels in the brain. Most patients present with headaches, focal neurological findings and focal seizures with or without generalisation. Our patient chiefly complained of an uncontrollable movement of her right hand that was initially fleeting but later became continuous. Her symptoms were initially described as tremors. We found an intracranial tumour as a cause of her symptoms, suspected the tumour to be a meningioma and performed surgical extirpation which resulted in symptom resolution...
June 1, 2022: JNMA; Journal of the Nepal Medical Association
https://read.qxmd.com/read/35595402/the-importance-of-timing-in-epilepsia-partialis-continua
#25
JOURNAL ARTICLE
Á Gutiérrez-Viedma, M Romeral-Jiménez, I Serrano-García, B Parejo-Carbonell, M L Cuadrado-Pérez, I Sanz-Graciani, I García-Morales
INTRODUCTION: Timing is one of the most important modifiable prognostic factors in the management of status epilepticus. Epilepsia partialis continua (EPC) is a status epilepticus subtype of highly variable, occasionally prolonged, duration. The aim of this study was to analyse the relationship between EPC duration and outcomes. METHODS: We performed an observational prospective study of all patients with EPC admitted to our tertiary hospital between 1 September 2017 and 1 September 2018...
May 2022: Neurología
https://read.qxmd.com/read/35509501/rituximab-in-rasmussen-s-encephalitis-a-single-center-experience-and-review-of-the-literature
#26
JOURNAL ARTICLE
Sujit A Jagtap, Sandeep Patil, Aniruddha Joshi, Nilesh Kurwale, Vivek Jain, Yogeshwari Deshmukh
Rasmussen's encephalitis (RE) is a rare chronic inflammatory disease of the brain resulting in unilateral hemispheric atrophy with drug-resistant focal epilepsy associated with a variable degree of progressive hemiparesis and cognitive decline. The precise etiology of RE is unknown but presumed to have a neuroinflammatory pathobiological basis. Only surgery halts progression of the disease, but may occur at the expense of a fixed but otherwise inevitable neurological deficit. Therefore, the question of medical management is an important consideration...
2022: Epilepsy & behavior reports
https://read.qxmd.com/read/35371717/epilepsia-partialis-continua-epc-as-an-uncommon-initial-presentation-of-cerebral-venous-sinus-thrombosis-cvst
#27
Yong Chuan Chee, Teck Cheng Yap
Cerebral venous sinus thrombosis (CVST) is a rare type of cerebrovascular disease that affects mainly young to middle-aged adults. The main clinical presentation of CVST includes progressive headache, focal neurological deficit, disturbance of conscious level, and epileptic seizures, which can occur early or late in the disease process. Generalized seizure has been recognised as the most common seizure subtype among patients with CVST and epileptic seizures. Epilepsia partialis continua (EPC), a subclass of focal motor status epilepticus, has rarely been reported as the initial presenting feature of CVST...
February 2022: Curēus
https://read.qxmd.com/read/34983160/rasmussen-s-encephalitis-a-rare-cause-of-intractable-seizures
#28
Muhammad Bilal Mazhar, Attiya Fatima, Muhammad Haroon Hamid
Rasmussen's encephalitis (RE) is a rare chronic progressive inflammatory disease of the brain that results in difficult-to-control seizures (mostly focal: epilepsia partialis continua), cognitive decline and progressive loss of neurological function including speech, motor skills with eventual paralysis of one half of the body (hemiparesis) and encephalitis. It is a disease that usually affects a single hemisphere and presents commonly at an early age. It poses a lot of challenges, both in diagnosis as well as treatment...
January 2022: Journal of the College of Physicians and Surgeons—Pakistan: JCPSP
https://read.qxmd.com/read/34959105/epilepsia-partialis-continua-in-relapsing-remitting-multiple-sclerosis-a-possible-distinct-relapse-phenotype
#29
JOURNAL ARTICLE
Justin Jain, Maksim Son, Derek B Debicki, Mandar Jog, Courtney S Casserly, Jorge G Burneo, Adrian Budhram
Epilepsia partialis continua (EPC) is a rare phenomenon in multiple sclerosis (MS). We describe a patient with relapsing-remitting MS and three episodes of EPC, with refractoriness to anti-seizure drugs but corticosteroid-responsiveness. No lesions likely attributable to her episodes of EPC were seen on 1.5 Tesla MRI, which we hypothesize was due to the small volume of presumed cortical/juxtacortical lesions involving the primary motor cortex. The association with relapsing-remitting disease, corticosteroid responsiveness, and dissemination of episodes of EPC in both space and time in our patient suggest that EPC may represent a distinct relapse phenotype in MS...
February 2022: Clinical Neurology and Neurosurgery
https://read.qxmd.com/read/34950404/recurrent-facial-focal-seizures-with-chronic-striatopathy-and-caudate-atrophy-a-double-whammy-in-an-elderly-woman-with-diabetes-mellitus
#30
Subhankar Chatterjee, Ritwik Ghosh, Umesh Kumar Ojha, Diksha, Payel Biswas, Julián Benito-León, Souvik Dubey
Seizures and involuntary movements are relatively rare, but well-known neurological complications of non-ketotic hyperglycemia. While hemichorea-hemiballism secondary to diabetic striatopathy is increasingly being reported, unilateral caudate atrophy resulting from chronic vascular insufficiency/insult in a backdrop of poorly controlled diabetes mellitus is sparsely described in literature. We herein report a 75-year-old woman with poorly controlled diabetes mellitus who presented with concurrent epilepsia partialis continua involving left side of her face and hemichorea on the right side in the context of non-ketotic hyperglycemia...
January 2022: Neurohospitalist
https://read.qxmd.com/read/34787083/epilepsia-partialis-continua-associated-with-the-p-arg403cys-variant-of-the-dnm1l-gene-an-unusual-clinical-progression-with-two-episodes-of-super-refractory-status-epilepticus-with-a-13-year-remission-interval
#31
Sara Minghetti, Roberto Giorda, Massimo Mastrangelo, Laura Tassi, Nicoletta Zanotta, Sara Galbiati, Maria Teresa Bassi, Claudio Zucca
Dynamin-1-like (DNM1L) is a gene located on chromosome 12p11.21 that encodes for dynamin-related protein (DRP1), a GTPase involved in mitochondrial and peroxisomal fusion, which plays a pivotal role in brain development. The missense variant, p.Arg403Cys, is clinically associated with childhood-onset super-refractory status epilepticus, with either subsequent poor neurological outcome or death (described in 13 patients). We present a 20-year-old girl carrying this mutation with a history of two episodes of super-refractory focal myoclonic status epilepticus which manifested as epilepsia partialis continua (EPC) with a 13-year interval, during which she displayed moderate intellectual disability, social and school reintegration, without complete control of myoclonic manifestations...
February 1, 2022: Epileptic Disorders: International Epilepsy Journal with Videotape
https://read.qxmd.com/read/34760781/subacute-measles-encephalitis-in-a-case-of-late-presenting-congenital-hiv-with-epilepsia-partialis-continua-as-the-first-manifestation-a-case-report
#32
Arka P Chakraborty, Adrija Ray, Debaleena Mukherjee, Subhadeep Gupta, Alak Pandit, Souvik Dubey
We report a case of a 14-year-old non-immunised girl with a prior history of measles infection presenting with afebrile seizures progressing to epilepsia partialis continua (EPC), quadriparesis and headache. Further evaluation revealed Human immunodeficiency virus (HIV) seropositivity with elevated anti-measles antibody titres in Cerebrospinal fluid (CSF). Electroencephalography showed focal epileptiform activity and Magnetic resonance imaging (MRI) of the brain revealed bilateral, asymmetrical long repetition time MRI (TR) hyperintensities involving juxtacortical white matter in both parietal lobes, left temporal and also in the left basal ganglia without any contrast enhancement or Diffusion weighted imaging (DWI) restriction...
September 2021: Journal of Family Medicine and Primary Care
https://read.qxmd.com/read/34760106/late-onset-epilepsia-partialis-continua-in-a-middle-aged-patient-with-huge-arachnoid-cyst
#33
Mohammad Javad Nasr, Amir Hossein Zohrevand, Ali Alizadeh Khatir
BACKGROUND: Arachnoid cysts are congenital or acquired cerebrospinal fluid (CSF) filled intra arachnoidal lesions, included 1% of all infantile intracranial masses and were discovered incidentally in MRI or CT-scan. The vast majority of these lesions are generally asymptomatic but some patients with arachnoid cyst have headache, dizziness, seizure (or epilepsy), vestibular symptoms and cognitive impairment. CASE PRESENTATION: We present a case of a 43-year-old woman who has late onset epilepsia partialis continua and had right spastic cerebral palsy due to huge arachnoid cyst...
2021: Caspian Journal of Internal Medicine
https://read.qxmd.com/read/34753808/-hand-mechanogram-in-epilepsia-partialis-continua
#34
JOURNAL ARTICLE
Philippe A Salles, Alberto J Espay
Epilepsia partialis continua manifests as low-frequency, rhythmic involuntary movements of a focal body part. We report a young man, HIV-positive and with syphilis, who developed right-hand epilepsia partialis continua associated with a small left-sided cortico-subcortical frontal lesion. A pen and paper test provided 'mechanographic' data on frequency, amplitude and rhythmicity of the hand movements, helping distinguish it from other causes of low-frequency repetitive hand movements.
December 2021: Practical Neurology
https://read.qxmd.com/read/34737526/epilepsia-partialis-continua-in-hyperosmolar-nonketotic-hyperglycemia
#35
JOURNAL ARTICLE
Rahul Rai, Pawan Dhull, Yogesh Kumar, Shaman Gill, Aneesh Mohimen, Amit S Nachankar
No abstract text is available yet for this article.
October 2021: Journal of Neurosciences in Rural Practice
https://read.qxmd.com/read/34730207/abdominal-epilepsia-partialis-continua-in-a-patient-with-astrocytoma-treated-with-lacosamide-value-of-repetitive-eeg-recordings
#36
JOURNAL ARTICLE
M Alemdar
OBJECTIVE: Isolated abdominal epilepsia partialis continua (EPC) without the involvement of other body parts is rarely seen. Abdominal EPC usually occurs either as a part of hemibody EPC or as an evolution of refractory EPC after initial treatment. As the isolated abdominal EPC was rarely reported up to date, the data regarding its pathophysiology and management are limited. Herein, we aimed to describe the clinical, neuroimaging, and electroencephalographic findings of a patient with abdominal EPC...
October 2021: European Review for Medical and Pharmacological Sciences
https://read.qxmd.com/read/34674208/crossed-cerebellar-diaschisis-in-eeg-negative-epilepsia-partialis-continua
#37
JOURNAL ARTICLE
Travis Larsh, Sumit Parikh
No abstract text is available yet for this article.
October 21, 2021: Neuropediatrics
https://read.qxmd.com/read/34401124/diagnosis-and-treatment-of-rasmussen-s-encephalitis-pose-a-big-challenge-two-case-reports-and-literature-review
#38
Ali Hammed, Maysaa Badour, Sameer Baqla, Fatema Amer
Rasmussen encephalitis (RE) is a rare disease of unknown etiology that causes severe chronic unihemispheric inflammatory disease of the central nervous system mainly in children. It leads to intractable seizures, cognitive decline and progressive neurological deficits in the affected hemisphere. We report two cases of RE, as defined by fulfillment of the 2005 Bien criteria. The diagnostic challenge of characterizing this rare disease will be highlighted by the extensive serum, CSF, MR imaging and EEG data in the two patients...
August 2021: Annals of Medicine and Surgery
https://read.qxmd.com/read/34015570/ictal-hypoperfusion-and-iron-deposition-in-the-symptomatogenic-zone-of-epilepsia-partialis-continua-a-case-report
#39
JOURNAL ARTICLE
Martin Schidlowski, Tobias Bauer, Bastian David, Felix Bitzer, Laura Ostermann, Attila Racz, Randi von Wrede, Alexander Radbruch, Tony Stöcker, Rainer Surges, Theodor Rüber
No abstract text is available yet for this article.
July 2021: Seizure: the Journal of the British Epilepsy Association
https://read.qxmd.com/read/33955717/responsive-neurostimulation-for-focal-motor-status-epilepticus
#40
JOURNAL ARTICLE
Jimmy C Yang, Nitish M Harid, Fábio A Nascimento, Vasileios Kokkinos, Abigail Shaughnessy, Alice D Lam, M Brandon Westover, Thabele M Leslie-Mazwi, Leigh R Hochberg, Eric S Rosenthal, Andrew J Cole, Robert M Richardson, Sydney S Cash
No clear evidence-based treatment paradigm currently exists for refractory and super-refractory status epilepticus, which can result in significant mortality and morbidity. While patients are typically treated with antiepileptic drugs and anesthetics, neurosurgical neuromodulation techniques can also be considered. We present a novel case in which responsive neurostimulation was used to effectively treat a patient who had developed super-refractory status epilepticus, later consistent with epilepsia partialis continua, that was refractory to antiepileptic drugs, immunomodulatory therapies, and transcranial magnetic stimulation...
June 2021: Annals of Clinical and Translational Neurology
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