Pierre Thoré, Xavier Jaïs, Laurent Savale, Peter Dorfmuller, Athénaïs Boucly, Matthieu Devilder, Olivier Meyrignac, Jérémie Pichon, Julie Mankikian, Marianne Riou, Emmanuel Boiffard, Clément Boissin, Pascal De Groote, Céline Chabanne, Frédéric Gagnadoux, Anne Bergeron, Nicolas Noel, Olivier Sitbon, Marc Humbert, David Montani
PURPOSE: Common variable immunodeficiency (CVID) is known to cause infectious, inflammatory, and autoimmune manifestations. Pulmonary hypertension (PH) is an unusual complication of CVID with largely unknown characteristics and mechanisms. METHODS: We report the clinical, functional, hemodynamics, radiologic and histologic characteristics, and outcomes of CVID-associated PH patients from the French PH Network. RESULTS: Ten patients were identified...
June 10, 2021: Journal of Clinical Immunology